{"id":97451,"date":"2017-10-26T10:46:43","date_gmt":"2017-10-26T15:46:43","guid":{"rendered":"https:\/\/www.erdheim-chester.org\/%e7%ac%ac%e4%ba%94%e5%b1%86%e5%b9%b4%e5%ba%a6-ecd-%e9%86%ab%e5%ad%b8%e7%a0%94%e8%a8%8e%e6%9c%83%ef%bc%8c%e7%b4%90%e7%b4%84%e5%b7%9e%e7%b4%90%e7%b4%84%e5%b8%82\/"},"modified":"2026-06-03T05:51:04","modified_gmt":"2026-06-03T10:51:04","slug":"%e7%ac%ac%e4%ba%94%e5%b1%86%e5%b9%b4%e5%ba%a6-ecd-%e9%86%ab%e5%ad%b8%e7%a0%94%e8%a8%8e%e6%9c%83%ef%bc%8c%e7%b4%90%e7%b4%84%e5%b7%9e%e7%b4%90%e7%b4%84%e5%b8%82","status":"publish","type":"post","link":"https:\/\/www.erdheim-chester.org\/zh-hant\/%e7%ac%ac%e4%ba%94%e5%b1%86%e5%b9%b4%e5%ba%a6-ecd-%e9%86%ab%e5%ad%b8%e7%a0%94%e8%a8%8e%e6%9c%83%ef%bc%8c%e7%b4%90%e7%b4%84%e5%b7%9e%e7%b4%90%e7%b4%84%e5%b8%82\/","title":{"rendered":"\u7b2c\u4e94\u5c46\u5e74\u5ea6 ECD \u91ab\u5b78\u7814\u8a0e\u6703\uff0c\u7d10\u7d04\u5dde\u7d10\u7d04\u5e02"},"content":{"rendered":"<p>[et_pb_section fb_built=&#8221;1&#8243; _builder_version=&#8221;4.27.6&#8243; 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locked=&#8221;off&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_row _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; width=&#8221;65%&#8221; width_tablet=&#8221;80%&#8221; width_phone=&#8221;80%&#8221; width_last_edited=&#8221;on|phone&#8221; custom_padding=&#8221;||0px||false|false&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_column type=&#8221;4_4&#8243; _builder_version=&#8221;4.27.5&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; custom_margin=&#8221;||15px||false|false&#8221; border_width_bottom=&#8221;2px&#8221; border_color_bottom=&#8221;#35A4BB&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;]<\/p>\n<h2>\u4ecb\u7d39<\/h2>\n<p>[\/et_pb_text][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;]\u4ee5\u4e0b\u65b0\u589e\u7684\u7c21\u5831\u5167\u5bb9\uff0c\u5e0c\u671b\u80fd\u5e6b\u52a9\u5176\u4ed6\u6709\u8208\u8da3\u9032\u4e00\u6b65\u77ad\u89e3 <a href=\"https:\/\/www.erdheim-chester.org\/zh-hant\/%e9%97%9c%e6%96%bc-ecd\/\">ECD<\/a> \u7684\u91ab\u5e2b\u8207\u7814\u7a76\u4eba\u54e1\u3002ECDGA \u611f\u8b1d\u91ab\u5b78\u754c\u70ba\u6539\u5584 ECD \u60a3\u8005\u7167\u8b77\u6240\u505a\u7684\u52aa\u529b\u8207\u8ca2\u737b\u3002[\/et_pb_text][et_pb_text module_class=&#8221;event-table&#8221; _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;]<\/p>\n\n<table id=\"tablepress-26\" class=\"tablepress tablepress-id-26\">\n<thead>\n<tr class=\"row-1\">\n\t<th class=\"column-1\">Presenter<\/th><th class=\"column-2\">Presentation Slides<\/th>\n<\/tr>\n<\/thead>\n<tbody class=\"row-striping row-hover\">\n<tr class=\"row-2\">\n\t<td class=\"column-1\">Ankush Bhatia, MD<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2018\/01\/Bhatia_Single-agent-dabrafenib-for-histiocytosis-10.24.2017-Final.pdf\" target=\"_blank\">Single-agent dabrafenib for BRAFV600E-mutated histiocytosis<\/a><\/td>\n<\/tr>\n<tr class=\"row-3\">\n\t<td class=\"column-1\">Riccardo Biavasco, MD<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2018\/01\/Biavasco_171026-BRAF-ECDGA.pdf\" target=\"_blank\">BRAFV600E expression in hematopoietic progenitors leads to myeloid skewing and histiocytosis<\/a><\/td>\n<\/tr>\n<tr class=\"row-4\">\n\t<td class=\"column-1\">Pascale Chasseur, MD<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2016\/11\/chasseur-Presentation4.pdf\" target=\"_blank\">A cytologic diagnosis of BRAFV600E Erdheim-Chester disease on pericardial fluid<\/a><\/td>\n<\/tr>\n<tr class=\"row-5\">\n\t<td class=\"column-1\">Marina Ferrarini, MD<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2016\/11\/Ferrarini_ECD-GA-2017.pdf\" target=\"_blank\">3-D culture of BRAF and KRAS-mutated Erdheim-Chester disease tissues: impact of kinase inhibitors<\/a><\/td>\n<\/tr>\n<tr class=\"row-6\">\n\t<td class=\"column-1\">Aaron Goodman, MD<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2016\/11\/Goodman-ECD-10-26-17.pdf\" target=\"_blank\">Genomics of Erdheim Chester Disease: Implications for Precision Treatment with Targeted Therapy<\/a><\/td>\n<\/tr>\n<tr class=\"row-7\">\n\t<td class=\"column-1\">Gaurav Goyal, MBBS<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2016\/11\/Goyal-ECD-biologics-Final.pdf\" target=\"_blank\">Efficacy of Biologic Agents in the Treatment of Erdheim-Chester Disease<\/a><\/td>\n<\/tr>\n<tr class=\"row-8\">\n\t<td class=\"column-1\">Gaurav Goyal, MBBS<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2016\/11\/Goyal-ECDGA-myeloid-neoplasm-10-25-2017.pdf\" target=\"_blank\">Increased prevalence of myeloid neoplasms in patients with Erdheim-Chester disease<\/a><\/td>\n<\/tr>\n<tr class=\"row-9\">\n\t<td class=\"column-1\">Julien Haroche, MD, PhD<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2016\/11\/Haroche-ECD_NY_26Oct2017.pdf\" target=\"_blank\">BRAF V600E mutation is associated with a cardiac and neurological phenotype in Erdheim-Chester disease: results from a 165-patient cohort<\/a><\/td>\n<\/tr>\n<tr class=\"row-10\">\n\t<td class=\"column-1\">Filip Janku, MD, PhD<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2016\/11\/Janku_ECD-NGS-2017.pdf\" target=\"_blank\">Clinical molecular profiling of archival tumor tissue and cell-free DNA from patients with Erdheim-Chester disease<\/a><\/td>\n<\/tr>\n<tr class=\"row-11\">\n\t<td class=\"column-1\">Augusto Vaglio, MD<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2016\/11\/Vaglio_Renal-ECD-Oct2017.pdf\" target=\"_blank\">Renal and ureteral involvement in Erdheim-Chester disease: analysis of a single centre cohort<\/a><\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n\n<p>[\/et_pb_text][\/et_pb_column][\/et_pb_row][et_pb_row _builder_version=&#8221;4.27.6&#8243; 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