{"id":102235,"date":"2019-04-01T18:26:07","date_gmt":"2019-04-01T23:26:07","guid":{"rendered":"https:\/\/www.erdheim-chester.org\/%e7%ac%ac%e4%b8%83%e5%b1%86%e5%b9%b4%e5%ba%a6%e5%b9%bc%e5%85%92%e7%99%bc%e5%b1%95%e9%86%ab%e5%ad%b8%e7%a0%94%e8%a8%8e%e6%9c%83%ef%bc%8c%e6%84%8f%e5%a4%a7%e5%88%a9%e7%b1%b3%e8%98%ad\/"},"modified":"2026-06-03T05:52:00","modified_gmt":"2026-06-03T10:52:00","slug":"%e7%ac%ac%e4%b8%83%e5%b1%86%e5%b9%b4%e5%ba%a6%e5%b9%bc%e5%85%92%e7%99%bc%e5%b1%95%e9%86%ab%e5%ad%b8%e7%a0%94%e8%a8%8e%e6%9c%83%ef%bc%8c%e6%84%8f%e5%a4%a7%e5%88%a9%e7%b1%b3%e8%98%ad","status":"publish","type":"post","link":"https:\/\/www.erdheim-chester.org\/zh-hant\/%e7%ac%ac%e4%b8%83%e5%b1%86%e5%b9%b4%e5%ba%a6%e5%b9%bc%e5%85%92%e7%99%bc%e5%b1%95%e9%86%ab%e5%ad%b8%e7%a0%94%e8%a8%8e%e6%9c%83%ef%bc%8c%e6%84%8f%e5%a4%a7%e5%88%a9%e7%b1%b3%e8%98%ad\/","title":{"rendered":"\u7b2c\u4e03\u5c46\u5e74\u5ea6\u5e7c\u5152\u767c\u5c55\u91ab\u5b78\u7814\u8a0e\u6703\uff0c\u610f\u5927\u5229\u7c73\u862d"},"content":{"rendered":"<p>[et_pb_section fb_built=&#8221;1&#8243; 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width_last_edited=&#8221;on|phone&#8221; custom_padding=&#8221;||0px||false|false&#8221; locked=&#8221;off&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_column type=&#8221;4_4&#8243; _builder_version=&#8221;4.27.5&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; custom_margin=&#8221;||15px||false|false&#8221; border_width_bottom=&#8221;2px&#8221; border_color_bottom=&#8221;#35A4BB&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;]<\/p>\n<h2>\u7814\u8a0e\u6703\u6458\u8981<\/h2>\n<p>[\/et_pb_text][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; hover_enabled=&#8221;0&#8243; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221; sticky_enabled=&#8221;0&#8243;]2019 \u5e74\u5e74\u5ea6 ECD \u91ab\u5b78\u7814\u8a0e\u6703\u7d04\u6709\u4f86\u81ea\u4e5d\u500b\u570b\u5bb6\u7684 38 \u4f4d\u91ab\u7642\u5c08\u696d\u4eba\u54e1\u51fa\u5e2d\u3002\u6703\u4e2d\u767c\u8868\u4e86 12 \u7bc7\u53e3\u982d\u6458\u8981\uff0c\u53e6\u6709 4 \u7bc7\u6d77\u5831\u5c55\u793a\u3002\u53d7\u9080\u8b1b\u8005 Luigi Naldini \u6559\u6388\u767c\u8868\u4e86\u984c\u70ba\u300c\u4ee5\u9020\u8840\u57fa\u56e0\u5de5\u7a0b\u6cbb\u7642   <\/p>\n<p>\u907a\u50b3\u6027\u75be\u75c5\u8207\u764c\u75c7\u300d\u7684\u6f14\u8b1b\u3002\u665a\u9593\u7684\u4ea4\u6d41\u9152\u6703\u63d0\u4f9b\u4e86\u8a0e\u8ad6\u6642\u9593\uff0c\u4fc3\u9032\u9019\u7fa4\u77e5\u8b58\u6df5\u535a\u3001\u5e0c\u671b\u9032\u4e00\u6b65\u4e86\u89e3 Erdheim-Chester Disease \u7684\u91ab\u5e2b\u8207\u79d1\u5b78\u5bb6\u4e4b\u9593\uff0c\u5c0d\u73fe\u6709\u53ca\u672a\u4f86\u5408\u4f5c\u7684\u652f\u6301\u3002[\/et_pb_text][\/et_pb_column][\/et_pb_row][et_pb_row _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; width=&#8221;65%&#8221; width_tablet=&#8221;80%&#8221; width_phone=&#8221;80%&#8221; width_last_edited=&#8221;on|phone&#8221; custom_padding=&#8221;||0px||false|false&#8221; locked=&#8221;off&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_column type=&#8221;4_4&#8243; _builder_version=&#8221;4.27.5&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; custom_margin=&#8221;||15px||false|false&#8221; border_width_bottom=&#8221;2px&#8221; border_color_bottom=&#8221;#35A4BB&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;]<\/p>\n<h2>\u51fa\u5e2d\u8005\u9ad4\u9a57<\/h2>\n<p>[\/et_pb_text][\/et_pb_column][\/et_pb_row][\/et_pb_section][et_pb_section fb_built=&#8221;1&#8243; _builder_version=&#8221;4.27.5&#8243; _module_preset=&#8221;default&#8221; custom_padding=&#8221;0px||||false|false&#8221; locked=&#8221;off&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_row column_structure=&#8221;1_2,1_2&#8243; _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; width=&#8221;65%&#8221; width_tablet=&#8221;80%&#8221; width_phone=&#8221;80%&#8221; width_last_edited=&#8221;on|phone&#8221; custom_padding=&#8221;0px||||false|false&#8221; locked=&#8221;off&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_column type=&#8221;1_2&#8243; _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;]<\/p>\n<p><em>\u300cECDGA \u70ba\u6211\u7684\u75c5\u60a3\u63d0\u4f9b\u4e86\u91cd\u8981\u7684<a href=\"https:\/\/www.erdheim-chester.org\/zh-hant\/%e8%b3%87%e6%ba%90\/\">\u8cc7\u6e90<\/a>\uff0c\u9032\u800c\u7e2e\u77ed\u4e86<a href=\"https:\/\/www.erdheim-chester.org\/zh-hant\/%e8%a8%ba%e6%96%b7\/\">\u8a3a\u65b7<\/a>\u6240\u9700\u7684\u6642\u9593\u3002\u5b83\u4e5f\u70ba\u7f55\u898b\u75be\u75c5\u60a3\u8005\u63d0\u4f9b\u4e86\u4e00\u500b\u793e\u7fa4\uff0c\u8b93\u4ed6\u5011\u4e0d\u518d\u611f\u5230\u5b64\u55ae\u3002\u300d <\/em><\/p>\n<p><strong>\u2013 Mark Heaney \u91ab\u5b78\u535a\u58eb\uff0c2019 \u5e74\u8207\u6703\u8005<\/strong><\/p>\n<p>[\/et_pb_text][\/et_pb_column][et_pb_column type=&#8221;1_2&#8243; 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_builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; width=&#8221;65%&#8221; width_tablet=&#8221;80%&#8221; width_phone=&#8221;80%&#8221; width_last_edited=&#8221;on|phone&#8221; custom_padding=&#8221;||0px||false|false&#8221; locked=&#8221;off&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_column type=&#8221;4_4&#8243; _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_image src=&#8221;https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2026\/03\/Picture1.png&#8221; title_text=&#8221;\u5716\u72471&#8243; _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][\/et_pb_image][\/et_pb_column][\/et_pb_row][et_pb_row _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; width=&#8221;65%&#8221; width_tablet=&#8221;80%&#8221; width_phone=&#8221;80%&#8221; width_last_edited=&#8221;on|phone&#8221; custom_padding=&#8221;||0px||false|false&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_column type=&#8221;4_4&#8243; _builder_version=&#8221;4.27.5&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; custom_margin=&#8221;||15px||false|false&#8221; border_width_bottom=&#8221;2px&#8221; border_color_bottom=&#8221;#35A4BB&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;]<\/p>\n<h2>\u4ecb\u7d39<\/h2>\n<p>[\/et_pb_text][et_pb_text module_class=&#8221;event-table&#8221; _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;]<\/p>\n\n<table id=\"tablepress-25\" class=\"tablepress tablepress-id-25\">\n<thead>\n<tr class=\"row-1\">\n\t<th class=\"column-1\">Presenter<\/th><th class=\"column-2\">Presentation Slides<\/th>\n<\/tr>\n<\/thead>\n<tbody class=\"row-striping row-hover\">\n<tr class=\"row-2\">\n\t<td class=\"column-1\">Jithma P. Abeykoon, MD<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2019\/10\/Ferrarini-3D-culture-of-BRAF-KRAS.pdf\" target=\"_blank\">Histopathologic Mimics of Erdheim-Chester Disease (ECD)<\/a><\/td>\n<\/tr>\n<tr class=\"row-3\">\n\t<td class=\"column-1\">Benjamin H. Durham<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2019\/10\/Durham-Novel-Alterations.pdf\" target=\"_blank\">Novel Alterations in CSF1R, RET, and Other Diverse Kinases in the Histiocytoses with Biochemical and Structural Insights into Their Mechanisms of Activation<\/a><\/td>\n<\/tr>\n<tr class=\"row-4\">\n\t<td class=\"column-1\">Marina Ferrarini, MD<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2019\/10\/Ferrarini-3D-culture-of-BRAF-KRAS.pdf\" target=\"_blank\">3D culture of BRAF\/KRAS-mutated Erdheim-Chester disease tissues unveils rewired histiocyte metabolism as new therapeutic target<\/a><\/td>\n<\/tr>\n<tr class=\"row-5\">\n\t<td class=\"column-1\">Filip Janku, MD, PhD<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2019\/10\/Janku-Trametinib.pdf\" target=\"_blank\">MEK inhibition with trametinib in patients with non-Langerhans cell histiocytosis irrespective of BRAF mutation status<\/a><\/td>\n<\/tr>\n<tr class=\"row-6\">\n\t<td class=\"column-1\">Francesco Pegoraro, MD<\/td><td class=\"column-2\"><a href=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2019\/10\/Pegoraro-Case-Study.pdf\" target=\"_blank\">Erdheim-Chester with multiple lesions related to BRAF V600E mutation. A simple coincidence?<\/a><\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<!-- #tablepress-25 from cache -->\n<p>[\/et_pb_text][\/et_pb_column][\/et_pb_row][et_pb_row _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; width=&#8221;65%&#8221; width_tablet=&#8221;80%&#8221; width_phone=&#8221;80%&#8221; width_last_edited=&#8221;on|phone&#8221; custom_padding=&#8221;||0px||false|false&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_column type=&#8221;4_4&#8243; _builder_version=&#8221;4.27.5&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; custom_margin=&#8221;||15px||false|false&#8221; border_width_bottom=&#8221;2px&#8221; border_color_bottom=&#8221;#35A4BB&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;]<\/p>\n<h2>\u7167\u7247<\/h2>\n<p>[\/et_pb_text][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; custom_margin=&#8221;20px||0px||false|false&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;]<\/p>\n<h3>\u62db\u5f85\u6703<\/h3>\n<p>[\/et_pb_text][et_pb_gallery gallery_ids=&#8221;32022,32574,32550,32538,32526,32514,32502,32490,32478,32466,32454,32442,32430,32418,32406,32394,32382,32370,32358,32346,32334,32322,32310,32298,32286,32274,32262,32250,32238,32226,32214,32202,32190,32178,32166,32154,32142,32130,32118,32106,32094,32082,32070,32058,32046,32034&#8243; posts_number=&#8221;100&#8243; orientation=&#8221;portrait&#8221; show_title_and_caption=&#8221;off&#8221; module_class=&#8221;event-gallery&#8221; _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; db_images_per_row=&#8221;5&#8243; db_image_max_width=&#8221;95%&#8221; db_image_max_height=&#8221;88px&#8221; db_image_row_spacing=&#8221;1%&#8221; dbdb_version=&#8221;5.1.1&#8243; db_image_object_fit=&#8221;cover&#8221; border_radii_image=&#8221;on|8px|8px|8px|8px&#8221; global_colors_info=&#8221;{}&#8221; theme_builder_area=&#8221;post_content&#8221;][\/et_pb_gallery][\/et_pb_column][\/et_pb_row][\/et_pb_section]<\/p>\n","protected":false},"excerpt":{"rendered":"<p>2019 \u5e74\u7c73\u862d\u91ab\u5b78\u7814\u8a0e\u6703\u5718\u9ad4\u5408\u7167 \u7814\u8a0e\u6703\u6458\u89812019 \u5e74\u5e74 [&hellip;]<\/p>\n","protected":false},"author":20,"featured_media":77437,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_et_pb_use_builder":"on","_et_pb_old_content":"","_et_gb_content_width":"","_wds_title":"","_wds_metadesc":"","_wds_focus-keywords":"","_wds_meta-robots-adv":"","_wds_meta-robots-noindex":false,"_wds_meta-robots-nofollow":false,"_wds_meta-robots-index":false,"_wds_meta-robots-follow":false,"_wds_autolinks-exclude":false,"_wds_canonical":"","_wds_redirect":"","_wds_opengraph":[],"_wds_twitter":[],"cybocfi_hide_featured_image":"","wds_primary_category":0,"footnotes":"","_links_to":"","_links_to_target":""},"categories":[4827],"tags":[],"class_list":["post-102235","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-4827"],"_links":{"self":[{"href":"https:\/\/www.erdheim-chester.org\/zh-hant\/wp-json\/wp\/v2\/posts\/102235","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.erdheim-chester.org\/zh-hant\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.erdheim-chester.org\/zh-hant\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/zh-hant\/wp-json\/wp\/v2\/users\/20"}],"replies":[{"embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/zh-hant\/wp-json\/wp\/v2\/comments?post=102235"}],"version-history":[{"count":20,"href":"https:\/\/www.erdheim-chester.org\/zh-hant\/wp-json\/wp\/v2\/posts\/102235\/revisions"}],"predecessor-version":[{"id":136460,"href":"https:\/\/www.erdheim-chester.org\/zh-hant\/wp-json\/wp\/v2\/posts\/102235\/revisions\/136460"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/zh-hant\/wp-json\/wp\/v2\/media\/77437"}],"wp:attachment":[{"href":"https:\/\/www.erdheim-chester.org\/zh-hant\/wp-json\/wp\/v2\/media?parent=102235"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/zh-hant\/wp-json\/wp\/v2\/categories?post=102235"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/zh-hant\/wp-json\/wp\/v2\/tags?post=102235"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}