{"id":50585,"date":"2019-03-10T12:09:48","date_gmt":"2019-03-10T16:09:48","guid":{"rendered":"https:\/\/www.erdheim-chester.org\/recursos-de-hematologia\/"},"modified":"2025-05-21T14:31:52","modified_gmt":"2025-05-21T18:31:52","slug":"recursos-de-hematologia","status":"publish","type":"page","link":"https:\/\/www.erdheim-chester.org\/pt-br\/recursos-de-hematologia\/","title":{"rendered":"Recursos de hematologia"},"content":{"rendered":"<p>[et_pb_section fb_built=&#8221;1&#8243; _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; background_image=&#8221;https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2024\/12\/Untitled-design-96-1.png&#8221; background_position=&#8221;bottom_center&#8221; background_vertical_offset=&#8221;20%&#8221; custom_padding=&#8221;20px||20px||true|false&#8221; background_last_edited=&#8221;on|desktop&#8221; background_position_tablet=&#8221;bottom_right&#8221; background_position_phone=&#8221;center_right&#8221; global_module=&#8221;28071&#8243; global_colors_info=&#8221;{}&#8221;][et_pb_row _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_column type=&#8221;4_4&#8243; _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_dmb_breadcrumbs _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; body_text_color=&#8221;#FFFFFF&#8221; body_font_size=&#8221;12px&#8221; link_text_color=&#8221;#35A4BB&#8221; custom_margin=&#8221;||5px||false|false&#8221; custom_padding=&#8221;||0px||false|false&#8221; body_font_size_tablet=&#8221;12px&#8221; body_font_size_phone=&#8221;10px&#8221; body_font_size_last_edited=&#8221;on|desktop&#8221; global_colors_info=&#8221;{}&#8221;][\/et_pb_dmb_breadcrumbs][et_pb_heading title=&#8221;@ET-DC@eyJkeW5hbWljIjp0cnVlLCJjb250ZW50IjoicG9zdF90aXRsZSIsInNldHRpbmdzIjp7ImJlZm9yZSI6IiIsImFmdGVyIjoiIn19@&#8221; _builder_version=&#8221;4.27.4&#8243; _dynamic_attributes=&#8221;title&#8221; _module_preset=&#8221;default&#8221; title_font=&#8221;&#8211;et_global_heading_font|300|||||||&#8221; title_text_color=&#8221;#FFFFFF&#8221; title_font_size=&#8221;40px&#8221; custom_margin=&#8221;||3px|||&#8221; title_font_size_tablet=&#8221;&#8221; title_font_size_phone=&#8221;25px&#8221; title_font_size_last_edited=&#8221;on|phone&#8221; global_colors_info=&#8221;{}&#8221;][\/et_pb_heading][et_pb_button button_url=&#8221;https:\/\/www.erdheim-chester.org\/pt-br\/entre-em-contato-conosco\/&#8221; button_text=&#8221;Entre em contato conosco&#8221; _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; custom_button=&#8221;on&#8221; button_text_size=&#8221;15px&#8221; button_text_color=&#8221;#C02E43&#8243; button_bg_color=&#8221;rgba(10,22,64,0.53)&#8221; button_border_width=&#8221;0px&#8221; button_icon=&#8221;&#xe60f;||divi||400&#8243; button_icon_color=&#8221;#C02E43&#8243; button_icon_placement=&#8221;left&#8221; button_on_hover=&#8221;off&#8221; global_colors_info=&#8221;{}&#8221; filter_opacity__hover_enabled=&#8221;on|hover&#8221; filter_opacity__hover=&#8221;70%&#8221;][\/et_pb_button][\/et_pb_column][\/et_pb_row][\/et_pb_section][et_pb_section fb_built=&#8221;1&#8243; admin_label=&#8221;section&#8221; _builder_version=&#8221;4.16&#8243; global_colors_info=&#8221;{}&#8221;][et_pb_row admin_label=&#8221;fila&#8221; _builder_version=&#8221;4.16&#8243; background_size=&#8221;initial&#8221; background_position=&#8221;top_left&#8221; background_repeat=&#8221;repeat&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_column type=&#8221;4_4&#8243; _builder_version=&#8221;4.16&#8243; custom_padding=&#8221;|||&#8221; global_colors_info=&#8221;{}&#8221; custom_padding__hover=&#8221;|||&#8221;][et_pb_text admin_label=&#8221;Text&#8221; _builder_version=&#8221;4.27.4&#8243; background_size=&#8221;initial&#8221; background_position=&#8221;top_left&#8221; background_repeat=&#8221;repeat&#8221; hover_enabled=&#8221;0&#8243; global_colors_info=&#8221;{}&#8221; sticky_enabled=&#8221;0&#8243;]<\/p>\n<p>ECD \u00e9 um tipo ultra-raro de c\u00e2ncer no sangue que \u00e9 dif\u00edcil de diagnosticar e pode se manifestar de v\u00e1rias formas complexas. Com a Erdheim-Chester A doen\u00e7a provavelmente est\u00e1 subdiagnosticada, e \u00e9 imperativo aumentar a conscientiza\u00e7\u00e3o em todo o mundo, especialmente na comunidade m\u00e9dica. Os hematologistas, juntamente com outros cl\u00ednicos, patologistas e radiologistas, desempenham um papel fundamental na identifica\u00e7\u00e3o da ECD. Se os m\u00e9dicos conseguirem reconhecer com precis\u00e3o e rapidez a ECD em um paciente, h\u00e1 tratamentos vi\u00e1veis, aprovados pela FDA e off-label, dispon\u00edveis para melhorar a qualidade de vida, retardar a progress\u00e3o da doen\u00e7a com risco de morte e, em alguns casos, at\u00e9 mesmo reverter os danos causados pelo dist\u00farbio. A chave para um resultado bem-sucedido ou mais positivo \u00e9 o diagn\u00f3stico precoce.    <\/p>\n<p>Agradecemos aos profissionais da \u00e1rea m\u00e9dica que forneceram as informa\u00e7\u00f5es e an\u00e1lises para apoiar os esfor\u00e7os de conscientiza\u00e7\u00e3o do site ECDGA. A dedica\u00e7\u00e3o de voc\u00eas \u00e0 comunidade far\u00e1 a diferen\u00e7a na vida de pacientes e fam\u00edlias em todos os lugares. <strong><br \/><img loading=\"lazy\" decoding=\"async\" class=\"alignright size-medium wp-image-20417\" src=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2022\/12\/ASH-2018-booth.jpg\" alt=\"\" width=\"300\" height=\"225\" srcset=\"https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2022\/12\/ASH-2018-booth.jpg 320w, https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2022\/12\/ASH-2018-booth-300x225.jpg 300w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><\/strong><\/p>\n<h2>Pontos-chave para hematologistas<\/h2>\n<ul>\n<li>Nenhuma das altera\u00e7\u00f5es patol\u00f3gicas \u00e9 exclusiva do site ECD &#8211; as caracter\u00edsticas cl\u00ednicas e radiogr\u00e1ficas s\u00e3o fundamentais para o diagn\u00f3stico.<\/li>\n<li>Um alto \u00edndice de suspeita para ECD em pacientes com envolvimento t\u00edpico de &#8220;rim piloso&#8221;, retroperitoneal ou \u00f3sseo, especialmente se houver diabetes ins\u00edpido concomitante.<\/li>\n<li>\u00c9 muito importante fazer um exame de PET-CT do v\u00e9rtice aos p\u00e9s (corpo inteiro) para capturar o envolvimento diametafis\u00e1rio ao redor da articula\u00e7\u00e3o do joelho e investigar o envolvimento de v\u00e1rios \u00f3rg\u00e3os.<\/li>\n<li>ECD pode coexistir com histiocitose de c\u00e9lulas de Langerhans (LCH) ou neoplasia mieloide.<\/li>\n<li>Os estudos moleculares desempenham um papel cada vez mais importante no diagn\u00f3stico e no gerenciamento.<\/li>\n<\/ul>\n<h2>ECD-Hematologistas experientes<\/h2>\n<p><strong>Ronald S. Go, MD<\/strong><br \/>E-mail: <a href=\"mailto:go.ronald@mayo.edu\">go.ronald@mayo.edu<\/a><\/p>\n<p><strong>Gaurav Goyal, MD<\/strong><br \/>E-mail: <a href=\"mailto:ggoyal@uabmc.edu\">ggoyal@uabmc.edu<\/a><\/p>\n<p><strong>Paul Hendrie, MD, PhD<\/strong><br \/>E-mail: <a href=\"mailto:phendrie@uw.edu\">phendrie@uw.edu<\/a><\/p>\n<p>[\/et_pb_text][\/et_pb_column][\/et_pb_row][\/et_pb_section]<\/p>\n","protected":false},"excerpt":{"rendered":"<p>[et_pb_dmb_breadcrumbs _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; body_text_color=&#8221;#FFFFFF&#8221; body_font_size=&#8221;12px&#8221; link_text_color=&#8221;#35A4BB&#8221; custom_margin=&#8221;||5px||false|false&#8221; custom_padding=&#8221;||0px||false|false&#8221; body_font_size_tablet=&#8221;12px&#8221; body_font_size_phone=&#8221;10px&#8221; body_font_size_last_edited=&#8221;on|desktop&#8221; global_colors_info=&#8221;{}&#8221;][\/et_pb_dmb_breadcrumbs]ECD \u00e9 um tipo ultra-raro de c\u00e2ncer no sangue que \u00e9 dif\u00edcil de diagnosticar e pode se manifestar de [&hellip;]<\/p>\n","protected":false},"author":14,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_et_pb_use_builder":"on","_et_pb_old_content":"","_et_gb_content_width":"","_wds_title":"","_wds_metadesc":"","_wds_focus-keywords":"","_wds_meta-robots-adv":"","_wds_meta-robots-noindex":false,"_wds_meta-robots-nofollow":false,"_wds_meta-robots-index":false,"_wds_meta-robots-follow":false,"_wds_autolinks-exclude":false,"_wds_canonical":"","_wds_redirect":"","_wds_opengraph":[],"_wds_twitter":[],"cybocfi_hide_featured_image":"","footnotes":"","_links_to":"","_links_to_target":""},"class_list":["post-50585","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.erdheim-chester.org\/pt-br\/wp-json\/wp\/v2\/pages\/50585","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.erdheim-chester.org\/pt-br\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.erdheim-chester.org\/pt-br\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/pt-br\/wp-json\/wp\/v2\/users\/14"}],"replies":[{"embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/pt-br\/wp-json\/wp\/v2\/comments?post=50585"}],"version-history":[{"count":0,"href":"https:\/\/www.erdheim-chester.org\/pt-br\/wp-json\/wp\/v2\/pages\/50585\/revisions"}],"wp:attachment":[{"href":"https:\/\/www.erdheim-chester.org\/pt-br\/wp-json\/wp\/v2\/media?parent=50585"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}