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admin_label=&#8221;section&#8221; _builder_version=&#8221;4.27.4&#8243; global_colors_info=&#8221;{}&#8221;][et_pb_row column_structure=&#8221;1_2,1_2&#8243; use_custom_gutter=&#8221;on&#8221; gutter_width=&#8221;2&#8243; _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; custom_padding=&#8221;||0px|0px|false|false&#8221; locked=&#8221;off&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_column type=&#8221;1_2&#8243; _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; background_color=&#8221;#F2F2F2&#8243; custom_padding=&#8221;40px|30px|40px|30px|true|false&#8221; border_radii=&#8221;on|20px|20px|20px|20px&#8221; box_shadow_style=&#8221;preset2&#8243; box_shadow_vertical=&#8221;4px&#8221; box_shadow_blur=&#8221;8px&#8221; box_shadow_color=&#8221;rgba(0,0,0,0.1)&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; custom_margin=&#8221;||||false|false&#8221; custom_padding=&#8221;0px||||false|false&#8221; border_radii=&#8221;on|20px|20px|20px|20px&#8221; border_width_all=&#8221;1px&#8221; border_color_all=&#8221;#adadad&#8221; global_colors_info=&#8221;{}&#8221;]<\/p>\n<div class=\"ecd-video-embed\">\n<div class=\"ecd-video-wrapper\">\n<iframe src=\"https:\/\/www.youtube.com\/embed\/videoseries?si=ABb7SJ7bffqiucQS&#038;list=PLd9i5JBvapc6OnYaLaArvVpWPtG6u0JAn\" title=\"\u092f\u0942\u091f\u094d\u092f\u0942\u092c \u0935\u0940\u0921\u093f\u092f\u094b \u092a\u094d\u0932\u0947\u092f\u0930\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture; web-share\" allowfullscreen=\"\"><\/iframe><\/div>\n<\/div>\n<p>[\/et_pb_text][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; custom_margin=&#8221;||||false|false&#8221; custom_padding=&#8221;||0px||false|false&#8221; hover_enabled=&#8221;0&#8243; global_colors_info=&#8221;{}&#8221; sticky_enabled=&#8221;0&#8243;]ECDGA YouTube \u092a\u094d\u0932\u0947\u0932\u093f\u0938\u094d\u091f \u092e\u0947\u0902 56 \u0935\u0940\u0921\u093f\u092f\u094b \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0902 \u091c\u093f\u0928\u092e\u0947\u0902 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u093e \u092a\u0947\u0936\u0947\u0935\u0930 Erdheim-Chester Disease (ECD) \u0915\u0947 \u0932\u093f\u090f \u0935\u0930\u094d\u0924\u092e\u093e\u0928 \u0909\u092a\u091a\u093e\u0930 \u0926\u0943\u0937\u094d\u091f\u093f\u0915\u094b\u0923\u094b\u0902 \u092a\u0930 \u091a\u0930\u094d\u091a\u093e \u0915\u0930\u0924\u0947 \u0939\u0948\u0902\u0964[\/et_pb_text][et_pb_button button_url=&#8221;https:\/\/www.youtube.com\/playlist?list=PLd9i5JBvapc6OnYaLaArvVpWPtG6u0JAn&#8221; url_new_window=&#8221;on&#8221; button_text=&#8221;\u092a\u094d\u0932\u0947\u0932\u093f\u0938\u094d\u091f \u0926\u0947\u0916\u0947\u0902&#8221; disabled_on=&#8221;off|off|off&#8221; _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; custom_button=&#8221;on&#8221; button_text_size=&#8221;16px&#8221; button_bg_color=&#8221;#C02E43&#8243; button_border_radius=&#8221;8px&#8221; button_font=&#8221;|600|||||||&#8221; button_use_icon=&#8221;off&#8221; transform_translate_linked__hover=&#8221;off&#8221; custom_padding=&#8221;16px|30px|16px|30px|true|true&#8221; custom_css_main_element=&#8221;width: 100%;||text-align: center;&#8221; locked=&#8221;off&#8221; global_colors_info=&#8221;{}&#8221; transform_styles__hover_enabled=&#8221;on|hover&#8221; transform_scale__hover_enabled=&#8221;on|desktop&#8221; transform_translate__hover_enabled=&#8221;on|hover&#8221; transform_rotate__hover_enabled=&#8221;on|desktop&#8221; transform_skew__hover_enabled=&#8221;on|desktop&#8221; transform_origin__hover_enabled=&#8221;on|desktop&#8221; transform_translate__hover=&#8221;0px|-3px&#8221; button_text_color__hover_enabled=&#8221;on|hover&#8221; button_text_color__hover=&#8221;#FFFFFF&#8221;][\/et_pb_button][\/et_pb_column][et_pb_column type=&#8221;1_2&#8243; _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221;]<\/p>\n<h3>\u0909\u092a\u091a\u093e\u0930 \u0938\u0902\u092c\u0902\u0927\u0940 \u0928\u093f\u0930\u094d\u0923\u092f<\/h3>\n<p>ECD \u0915\u0947 \u0932\u093f\u090f \u0909\u091a\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 \u0915\u093e \u0928\u093f\u0930\u094d\u0923\u092f \u0932\u0947\u0928\u0947 \u092e\u0947\u0902 \u0930\u094b\u0917\u0940 \u0914\u0930 \u0909\u0928\u0915\u0947 \u0921\u0949\u0915\u094d\u091f\u0930\u094b\u0902 \u0915\u0947 \u092c\u0940\u091a \u0938\u0939\u092f\u094b\u0917 \u0936\u093e\u092e\u093f\u0932 \u0939\u094b\u0924\u093e \u0939\u0948\u0964 \u0926\u0947\u0936 \u0914\u0930 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u0915 \u0915\u0947 \u0905\u0928\u0941\u092d\u0935 \u0915\u0947 \u0906\u0927\u093e\u0930 \u092a\u0930 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u093e \u0909\u092a\u091a\u093e\u0930 \u092d\u093f\u0928\u094d\u0928 \u0939\u094b \u0938\u0915\u0924\u093e \u0939\u0948\u0964 \u0939\u093e\u0932\u093e\u0902\u0915\u093f, \u0905\u0927\u093f\u0915\u093e\u0902\u0936 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u0915 <em><i>Blood<\/i><\/em> \u092e\u0947\u0902 \u092f\u093e National Comprehensive Cancer Network\u00ae (NCCN\u00ae) \u0926\u094d\u0935\u093e\u0930\u093e \u092a\u094d\u0930\u0915\u093e\u0936\u093f\u0924 \u0938\u0930\u094d\u0935\u0938\u092e\u094d\u092e\u0924\u093f \u0938\u093f\u092b\u093e\u0930\u093f\u0936\u094b\u0902 \u092a\u0930 \u0928\u093f\u0930\u094d\u092d\u0930 \u0915\u0930\u0924\u0947 \u0939\u0948\u0902\u0964 \u0907\u0928 \u0938\u093f\u092b\u093e\u0930\u093f\u0936\u094b\u0902 \u092e\u0947\u0902 \u0915\u0939\u093e \u0917\u092f\u093e \u0939\u0948 \u0915\u093f \u0909\u092a\u091a\u093e\u0930 \u0930\u094b\u0917 \u0915\u0947 \u092c\u094b\u091d (\u0936\u0930\u0940\u0930 \u0915\u0947 \u0915\u094c\u0928 \u0938\u0947 \u0939\u093f\u0938\u094d\u0938\u0947 ECD \u0938\u0947 \u092a\u094d\u0930\u092d\u093e\u0935\u093f\u0924 \u0939\u0948\u0902), \u0909\u0924\u094d\u092a\u0930\u093f\u0935\u0930\u094d\u0924\u0928 \u0915\u0940 \u0938\u094d\u0925\u093f\u0924\u093f, \u0926\u0935\u093e \u0915\u0940 \u0909\u092a\u0932\u092c\u094d\u0927\u0924\u093e \u0914\u0930 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u0915 \u0915\u0947 \u0905\u0928\u0941\u092d\u0935 \u092a\u0930 \u0928\u093f\u0930\u094d\u092d\u0930 \u0915\u0930\u0924\u093e \u0939\u0948\u0964   <\/p>\n<h3>\u0909\u092a\u091a\u093e\u0930 \u0915\u093e \u091a\u092f\u0928<\/h3>\n<p>\u0938\u094c\u092d\u093e\u0917\u094d\u092f \u0938\u0947, ECD \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u092a\u093e\u0938 \u0909\u092a\u091a\u093e\u0930 \u0915\u0947 \u0935\u093f\u0915\u0932\u094d\u092a \u0939\u0948\u0902, \u091c\u093f\u0928\u092e\u0947\u0902 \u0938\u0947 \u0915\u0941\u091b \u0905\u0927\u093f\u0915\u093e\u0902\u0936 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u092c\u0939\u0941\u0924 \u092a\u094d\u0930\u092d\u093e\u0935\u0940 \u0938\u093e\u092c\u093f\u0924 \u0939\u0941\u090f \u0939\u0948\u0902\u0964 \u092c\u093f\u0928\u093e \u0932\u0915\u094d\u0937\u0923\u094b\u0902 \u0935\u093e\u0932\u0947 \u0915\u0941\u091b \u0930\u094b\u0917\u0940, \u091c\u093f\u0928\u094d\u0939\u0947\u0902 &#8220;\u0938\u094d\u092a\u0930\u094d\u0936\u094b\u0928\u094d\u092e\u0941\u0916 \u0930\u094b\u0917&#8221; \u0915\u0947 \u0930\u0942\u092a \u092e\u0947\u0902 \u092d\u0940 \u091c\u093e\u0928\u093e \u091c\u093e\u0924\u093e \u0939\u0948, \u0914\u0930 \u091c\u093f\u0928\u092e\u0947\u0902 ECD \u092a\u094d\u0930\u092e\u0941\u0916 \u0905\u0902\u0917\u094b\u0902 \u0915\u094b \u092a\u094d\u0930\u092d\u093e\u0935\u093f\u0924 \u0928\u0939\u0940\u0902 \u0915\u0930\u0924\u093e \u0939\u0948, \u0935\u0947 \u092c\u093f\u0928\u093e \u0915\u093f\u0938\u0940 \u0909\u092a\u091a\u093e\u0930 \u0915\u0947 \u0928\u093f\u0917\u0930\u093e\u0928\u0940 \u0914\u0930 \u092a\u094d\u0930\u0924\u0940\u0915\u094d\u0937\u093e \u0915\u0940 \u0905\u0935\u0927\u093f \u092e\u0947\u0902 \u092a\u094d\u0930\u0935\u0947\u0936 \u0915\u0930 \u0938\u0915\u0924\u0947 \u0939\u0948\u0902\u0964 \u0939\u093e\u0932\u093e\u0902\u0915\u093f, \u0909\u092a\u091a\u093e\u0930 \u0915\u0940 \u0906\u092e \u0924\u094c\u0930 \u092a\u0930 \u0938\u093f\u092b\u093e\u0930\u093f\u0936 \u0915\u0940 \u091c\u093e\u0924\u0940 \u0939\u0948, \u0935\u093f\u0936\u0947\u0937 \u0930\u0942\u092a \u0938\u0947 \u0909\u0928 \u0932\u094b\u0917\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u091c\u093f\u0928\u092e\u0947\u0902 \u092e\u0939\u0924\u094d\u0935\u092a\u0942\u0930\u094d\u0923 \u0905\u0902\u0917 \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0902, \u091c\u0948\u0938\u0947 \u0939\u0943\u0926\u092f \u092f\u093e \u0915\u0947\u0902\u0926\u094d\u0930\u0940\u092f \u0924\u0902\u0924\u094d\u0930\u093f\u0915\u093e \u0924\u0902\u0924\u094d\u0930\u0964  <\/p>\n<p>[\/et_pb_text][\/et_pb_column][\/et_pb_row][et_pb_row column_structure=&#8221;1_2,1_2&#8243; use_custom_gutter=&#8221;on&#8221; gutter_width=&#8221;2&#8243; _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_column type=&#8221;1_2&#8243; _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_image src=&#8221;https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2025\/02\/Treatment-list-graphic-for-website.jpg&#8221; title_text=&#8221;\u0909\u092a\u091a\u093e\u0930 \u0938\u0942\u091a\u0940 &#8211; \u0935\u0947\u092c\u0938\u093e\u0907\u091f \u0915\u0947 \u0932\u093f\u090f \u0917\u094d\u0930\u093e\u092b\u093c\u093f\u0915&#8221; show_in_lightbox=&#8221;on&#8221; _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; custom_margin=&#8221;||0px||false|false&#8221; global_colors_info=&#8221;{}&#8221;][\/et_pb_image][et_pb_button button_url=&#8221;https:\/\/www.erdheim-chester.org\/wp-content\/uploads\/2025\/02\/Treatment-list-graphic-for-website.pdf&#8221; url_new_window=&#8221;on&#8221; button_text=&#8221;\u092a\u0940\u0921\u0940\u090f\u092b \u0921\u093e\u0909\u0928\u0932\u094b\u0921 \u0915\u0930\u0947\u0902&#8221; module_class=&#8221;full-button&#8221; _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; custom_padding=&#8221;10px||10px||true|false&#8221; global_colors_info=&#8221;{}&#8221;][\/et_pb_button][\/et_pb_column][et_pb_column type=&#8221;1_2&#8243; _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221;]<\/p>\n<h3>\u0909\u092a\u091a\u093e\u0930 \u092c\u0928\u093e\u092e \u0907\u0932\u093e\u091c<\/h3>\n<p>\u0939\u093e\u0932\u093e\u0901\u0915\u093f ECD \u0915\u0947 \u0932\u093f\u090f \u092a\u094d\u0930\u092d\u093e\u0935\u0940 \u0909\u092a\u091a\u093e\u0930 \u092e\u094c\u091c\u0942\u0926 \u0939\u0948\u0902, \u0932\u0947\u0915\u093f\u0928 \u0907\u0938\u0915\u093e \u0907\u0932\u093e\u091c \u0905\u092d\u0940 \u0924\u0915 \u0928\u0939\u0940\u0902 \u092e\u093f\u0932 \u092a\u093e\u092f\u093e \u0939\u0948\u0964 \u0906\u091c \u0909\u092a\u0932\u092c\u094d\u0927 \u0938\u0930\u094d\u0935\u094b\u0924\u094d\u0924\u092e \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u094b \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 \u0915\u0939\u093e \u091c\u093e\u0924\u093e \u0939\u0948 \u0914\u0930 \u092f\u0947 \u0906\u092e\u0924\u094c\u0930 \u092a\u0930 ECD \u0918\u093e\u0935\u094b\u0902 \u0915\u094b \u0928\u093f\u092f\u0902\u0924\u094d\u0930\u093f\u0924 \u0915\u0930\u0928\u0947 \u0914\u0930 \u0905\u0915\u094d\u0938\u0930 \u0915\u092e \u0915\u0930\u0928\u0947 \u092e\u0947\u0902 \u0938\u092b\u0932 \u0939\u094b\u0924\u0947 \u0939\u0948\u0902\u0964 \u0935\u0930\u094d\u0924\u092e\u093e\u0928 \u092e\u0947\u0902, \u0907\u0928 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u094b \u0906\u092e \u0924\u094c\u0930 \u092a\u0930 \u0905\u0928\u093f\u0936\u094d\u091a\u093f\u0924 \u0915\u093e\u0932 \u0924\u0915 \u091c\u093e\u0930\u0940 \u0930\u0916\u0928\u093e \u091a\u093e\u0939\u093f\u090f, \u092f\u093e \u092c\u0940\u092e\u093e\u0930\u0940 \u0915\u0947 \u092b\u093f\u0930 \u0938\u0947 \u092c\u0922\u093c\u0928\u0947 \u0915\u0940 \u0938\u0902\u092d\u093e\u0935\u0928\u093e \u0939\u0948\u0964 \u0939\u093e\u0932\u093e\u0901\u0915\u093f, \u0938\u092b\u0932 \u0909\u092a\u091a\u093e\u0930 \u0915\u0947 \u0938\u093e\u0925, ECD \u0905\u0915\u094d\u0938\u0930 \u090f\u0915 \u092a\u0941\u0930\u093e\u0928\u0940 \u092c\u0940\u092e\u093e\u0930\u0940 \u0915\u0947 \u0930\u0942\u092a \u092e\u0947\u0902 \u0928\u093f\u092f\u0902\u0924\u094d\u0930\u093f\u0924 \u0915\u093f\u092f\u093e \u091c\u093e \u0938\u0915\u0924\u093e \u0939\u0948\u0964   <\/p>\n<h3>\u0909\u092a\u091a\u093e\u0930 \u0915\u0947 \u092a\u094d\u0930\u0915\u093e\u0930<\/h3>\n<p>\u0935\u093f\u0936\u093f\u0937\u094d\u091f ECD \u0909\u092a\u091a\u093e\u0930 \u0924\u0940\u0928 \u0936\u094d\u0930\u0947\u0923\u093f\u092f\u094b\u0902 \u092e\u0947\u0902 \u0938\u0947 \u090f\u0915 \u092e\u0947\u0902 \u0906\u0924\u0947 \u0939\u0948\u0902: (1) \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930, (2) \u0915\u0940\u092e\u094b\u0925\u0947\u0930\u0947\u092a\u0940, \u092f\u093e (3) \u0907\u092e\u094d\u092f\u0942\u0928\u094b\u0925\u0947\u0930\u0947\u092a\u0940\u0964 \u092f\u0939 \u0938\u093e\u0930\u094d\u0935\u092d\u094c\u092e\u093f\u0915 \u0930\u0942\u092a \u0938\u0947 \u0938\u094d\u0925\u093e\u092a\u093f\u0924 \u0939\u0948 \u0915\u093f \u0932\u0915\u094d\u0937\u093f\u0924 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u093e \u0928\u094d\u092f\u0942\u0930\u094b\u0932\u0949\u091c\u093f\u0915\u0932 \u092f\u093e \u0939\u0943\u0926\u092f \u0930\u094b\u0917 \u0935\u093e\u0932\u0947 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u094b \u0924\u092c \u0926\u0940 \u091c\u093e\u0928\u0940 \u091a\u093e\u0939\u093f\u090f \u091c\u092c \u0930\u094b\u0917\u0940 \u0915\u0947 \u0926\u0947\u0936 \u092e\u0947\u0902 \u0909\u092a\u0932\u092c\u094d\u0927 \u0939\u094b\u0964 \u0905\u0928\u094d\u092f \u092a\u0930\u093f\u0938\u094d\u0925\u093f\u0924\u093f\u092f\u094b\u0902 \u092e\u0947\u0902, \u0928\u093f\u092e\u094d\u0928\u0932\u093f\u0916\u093f\u0924 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u092a\u0930 \u0935\u093f\u091a\u093e\u0930 \u0915\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0939\u0948 \u0914\u0930\/\u092f\u093e \u0909\u0928\u0915\u0940 \u0938\u093f\u092b\u093e\u0930\u093f\u0936 \u0915\u0940 \u091c\u093e\u0924\u0940 \u0939\u0948:  <\/p>\n<ul>\n<li>\u092a\u094d\u0930\u0924\u093f\u0930\u0915\u094d\u0937\u093e-\u0938\u0902\u0936\u094b\u0927\u093f\u0924 \u0909\u092a\u091a\u093e\u0930<\/li>\n<\/ul>\n<ul>\n<li style=\"list-style-type: none;\">\n<ul>\n<li>Interferon \u092f\u093e peginterferon<\/li>\n<li>mTOR inhibitor: everolimus, sirolimus<\/li>\n<li>Cytokine inhibitor: anakinra, tocilizumab <\/li>\n<\/ul>\n<\/li>\n<li>\u0915\u0940\u092e\u094b\u0925\u0947\u0930\u092a\u0940\n<ul>\n<li>Cladribine<\/li>\n<li>Cytarabine<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<p>\u0930\u094b\u0917\u0940 \u0915\u0947 <a href=\"https:\/\/www.erdheim-chester.org\/hi\/%e0%a4%b2%e0%a4%95%e0%a5%8d%e0%a4%b7%e0%a4%a3\/\"><u>\u0932\u0915\u094d\u0937\u0923\u094b\u0902<\/u><\/a> \u0914\u0930 \u0938\u0939\u0930\u0941\u0917\u094d\u0923\u0924\u093e\u0913\u0902 \u0915\u0947 \u0906\u0927\u093e\u0930 \u092a\u0930 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u0915 \u0915\u0947 \u0938\u093e\u0925 \u0907\u0928 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u092a\u0930 \u091a\u0930\u094d\u091a\u093e \u0915\u0940 \u091c\u093e\u0928\u0940 \u091a\u093e\u0939\u093f\u090f\u0964<\/p>\n<p>[\/et_pb_text][\/et_pb_column][\/et_pb_row][et_pb_row _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; custom_padding=&#8221;||1px|||&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_column type=&#8221;4_4&#8243; _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_text admin_label=&#8221;Text&#8221; _builder_version=&#8221;4.27.6&#8243; background_size=&#8221;initial&#8221; background_position=&#8221;top_left&#8221; background_repeat=&#8221;repeat&#8221; global_colors_info=&#8221;{}&#8221;]<\/p>\n<h3>\u0932\u0915\u094d\u0937\u093f\u0924 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u093e<\/h3>\n<p>\u092f\u0947 ECD \u0915\u0947 \u0932\u093f\u090f \u0909\u092a\u0932\u092c\u094d\u0927 \u0928\u0935\u0940\u0928\u0924\u092e \u0914\u0930 \u0906\u092e \u0924\u094c\u0930 \u092a\u0930 \u0938\u092c\u0938\u0947 \u0906\u0936\u093e\u091c\u0928\u0915 \u0909\u092a\u091a\u093e\u0930 \u0939\u0948\u0902\u0964 \u092f\u0947 \u0906\u092e \u0924\u094c\u0930 \u092a\u0930 \u0905\u0927\u093f\u0915\u093e\u0902\u0936 \u0905\u0902\u0917\u094b\u0902 \u092e\u0947\u0902 ECD \u0915\u0940 \u092a\u094d\u0930\u0917\u0924\u093f \u0915\u094b \u0930\u094b\u0915\u0924\u0947 \u0939\u0948\u0902, \u0939\u093e\u0932\u093e\u0902\u0915\u093f \u092e\u0938\u094d\u0924\u093f\u0937\u094d\u0915 \u0915\u0940 \u092d\u093e\u0917\u0940\u0926\u093e\u0930\u0940 \u0915\u094b \u092c\u0939\u0941\u0924 \u0938\u093e\u0935\u0927\u093e\u0928\u0940 \u0938\u0947 \u0926\u0947\u0916\u093e \u091c\u093e\u0928\u093e \u091a\u093e\u0939\u093f\u090f\u0964 \u0915\u0941\u091b \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f, \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u0930\u0915\u094d\u0924\/\u092e\u0938\u094d\u0924\u093f\u0937\u094d\u0915 \u092c\u093e\u0927\u093e \u0915\u094b \u092a\u093e\u0930 \u0915\u0930\u0928\u093e \u0914\u0930 \u092e\u0938\u094d\u0924\u093f\u0937\u094d\u0915 \u0924\u0915 \u0926\u0935\u093e \u092a\u0939\u0941\u0902\u091a\u093e\u0928\u093e \u092e\u0941\u0936\u094d\u0915\u093f\u0932 \u0939\u094b \u0938\u0915\u0924\u093e \u0939\u0948, \u091c\u093f\u0938\u0938\u0947 \u092e\u0938\u094d\u0924\u093f\u0937\u094d\u0915 \u092e\u0947\u0902 ECD \u0915\u0940 \u092a\u094d\u0930\u0917\u0924\u093f \u0915\u094b \u0930\u094b\u0915\u0928\u0947 \u092e\u0947\u0902 \u0909\u0928\u0915\u0940 \u092a\u094d\u0930\u092d\u093e\u0935\u0936\u0940\u0932\u0924\u093e \u0915\u092e \u0939\u094b \u091c\u093e\u0924\u0940 \u0939\u0948\u0964 \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 \u092e\u0939\u0902\u0917\u0947 \u0939\u0948\u0902 \u0914\u0930 \u0926\u0941\u0928\u093f\u092f\u093e \u0915\u0947 \u0915\u0941\u091b \u0939\u093f\u0938\u094d\u0938\u094b\u0902 \u092e\u0947\u0902 \u092a\u094d\u0930\u093e\u092a\u094d\u0924 \u0915\u0930\u0928\u093e \u091a\u0941\u0928\u094c\u0924\u0940\u092a\u0942\u0930\u094d\u0923 \u0939\u094b \u0938\u0915\u0924\u093e \u0939\u0948\u0964   <\/p>\n<p>ECD \u092e\u0947\u0902 \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 \u0938\u0902\u0935\u0948\u0927\u093e\u0928\u093f\u0915 \u0938\u0915\u094d\u0930\u093f\u092f\u0923 \u090f\u092e\u090f\u092a\u0940 \u0915\u093f\u0928\u0947\u0938\u0947\u0938 \u092e\u093e\u0930\u094d\u0917 \u0915\u0948\u0938\u094d\u0915\u0947\u0921 \u0915\u094b \u0905\u0935\u0930\u0941\u0926\u094d\u0927 \u0915\u0930\u0924\u0947 \u0939\u0948\u0902, \u091c\u094b ECD \u0915\u0947 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u092e\u0947\u0902 \u092e\u094c\u091c\u0942\u0926 \u0935\u093f\u092d\u093f\u0928\u094d\u0928 \u090f\u092e\u090f\u092a\u0940\u0915\u0947 \u092e\u093e\u0930\u094d\u0917 \u0909\u0924\u094d\u092a\u0930\u093f\u0935\u0930\u094d\u0924\u0928\u094b\u0902 \u0915\u094b \u0938\u0902\u092c\u094b\u0927\u093f\u0924 \u0915\u0930\u0924\u0947 \u0939\u0948\u0902\u0964 \u0932\u0915\u094d\u0937\u093f\u0924 \u090f\u091c\u0947\u0902\u091f \u0915\u093e \u091a\u0941\u0928\u093e\u0935 \u0905\u0915\u094d\u0938\u0930 \u0906\u0928\u0941\u0935\u0902\u0936\u093f\u0915 \u092a\u0930\u0940\u0915\u094d\u0937\u0923 \u0915\u0947 \u0906\u0927\u093e\u0930 \u092a\u0930 ECD \u090a\u0924\u0915 \u092e\u0947\u0902 \u092e\u094c\u091c\u0942\u0926 \u0909\u0924\u094d\u092a\u0930\u093f\u0935\u0930\u094d\u0924\u0928\u094b\u0902 \u0926\u094d\u0935\u093e\u0930\u093e \u0928\u093f\u0930\u094d\u0926\u0947\u0936\u093f\u0924 \u0939\u094b\u0924\u093e \u0939\u0948\u0964 <\/p>\n<ul>\n<li><strong><em><b>BRAF V600E<\/b><\/em><\/strong><strong>-\u0909\u0924\u094d\u092a\u0930\u093f\u0935\u0930\u094d\u0924\u093f\u0924 ECD<\/strong><br \/>\u0932\u0917\u092d\u0917 50% \u0930\u094b\u0917\u0940 <em><i>BRAF V600E<\/i><\/em> \u0915\u0947 \u0932\u093f\u090f \u0938\u0915\u093e\u0930\u093e\u0924\u094d\u092e\u0915 <a href=\"https:\/\/www.erdheim-chester.org\/hi\/?page_id=130913\"><u>\u092a\u0930\u0940\u0915\u094d\u0937\u0923<\/u> <\/a> \u0915\u0930\u0947\u0902\u0917\u0947\u0964 \u0907\u0928 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u0909\u092a\u091a\u093e\u0930 \u0935\u093f\u0915\u0932\u094d\u092a\u094b\u0902 \u092e\u0947\u0902 \u0906\u092e \u0924\u094c\u0930 \u092a\u0930 BRAF inhibitor, <em>MEK<\/em> inhibitor, \u092f\u093e \u0926\u094b\u0928\u094b\u0902 \u0915\u093e \u0938\u0902\u092f\u094b\u091c\u0928 (\u0926\u0941\u0930\u094d\u0932\u092d \u092e\u093e\u092e\u0932\u094b\u0902 \u092e\u0947\u0902) \u0936\u093e\u092e\u093f\u0932 \u0939\u094b\u0924\u093e \u0939\u0948\u0964 \u0906\u092e\u0924\u094c\u0930 \u092a\u0930 \u0909\u092a\u092f\u094b\u0917 \u0915\u093f\u090f \u091c\u093e\u0928\u0947 \u0935\u093e\u0932\u0947 BRAF inhibitors \u092e\u0947\u0902 vemurafenib, dabrafenib \u0914\u0930 encorafenib \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0902\u0964 \u0906\u092e\u0924\u094c\u0930 \u092a\u0930 \u0909\u092a\u092f\u094b\u0917 \u0915\u093f\u090f \u091c\u093e\u0928\u0947 \u0935\u093e\u0932\u0947 MEK inhibitors \u092e\u0947\u0902 cobimetinib, trametinib, binimetinib \u0914\u0930 selumetinib \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0902\u0964 USA \u092e\u0947\u0902, vemurafenib \u0914\u0930 cobimetinib ECD \u0915\u0947 \u0932\u093f\u090f FDA-\u0905\u0928\u0941\u092e\u094b\u0926\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 \u0939\u0948\u0902\u0964   <\/li>\n<li><strong>ECD \u092c\u093f\u0928\u093e <\/strong><strong><em>BRAF V600E<\/em><\/strong><strong> \u0909\u0924\u094d\u092a\u0930\u093f\u0935\u0930\u094d\u0924\u0928 \u0915\u0947<\/strong><br \/>\u0905\u0927\u093f\u0915\u093e\u0902\u0936 \u0930\u094b\u0917\u0940 \u091c\u094b <em><i>BRAF V600E<\/i><\/em> \u0909\u0924\u094d\u092a\u0930\u093f\u0935\u0930\u094d\u0924\u0928 \u0915\u0947 \u0932\u093f\u090f \u0928\u0915\u093e\u0930\u093e\u0924\u094d\u092e\u0915 <a href=\"https:\/\/www.erdheim-chester.org\/hi\/?page_id=130913\"><u>\u092a\u0930\u0940\u0915\u094d\u0937\u0923<\/u><\/a> \u0915\u0930\u0924\u0947 \u0939\u0948\u0902, \u0909\u0928\u092e\u0947\u0902 MAPK pathway (\u091c\u093f\u0938\u0947 Ras-Raf-MEK-ERK pathway \u0915\u0947 \u0930\u0942\u092a \u092e\u0947\u0902 \u092d\u0940 \u091c\u093e\u0928\u093e \u091c\u093e\u0924\u093e \u0939\u0948) \u092e\u0947\u0902 \u090f\u0915 \u0905\u0932\u0917 \u0909\u0924\u094d\u092a\u0930\u093f\u0935\u0930\u094d\u0924\u0928 \u0939\u094b\u0917\u093e\u0964 \u092f\u0939 pathway \u0915\u094b\u0936\u093f\u0915\u093e \u092e\u0947\u0902 \u092a\u094d\u0930\u094b\u091f\u0940\u0928 \u0915\u0940 \u090f\u0915 \u0936\u094d\u0930\u0943\u0902\u0916\u0932\u093e \u0939\u0948 \u091c\u094b \u0915\u094b\u0936\u093f\u0915\u093e \u0915\u0940 \u0938\u0924\u0939 \u092a\u0930 \u090f\u0915 \u0930\u093f\u0938\u0947\u092a\u094d\u091f\u0930 \u0938\u0947 \u0915\u094b\u0936\u093f\u0915\u093e \u0915\u0947 \u0928\u093e\u092d\u093f\u0915 \u092e\u0947\u0902 DNA \u0924\u0915 \u090f\u0915 \u0938\u0902\u0915\u0947\u0924 \u0938\u0902\u091a\u093e\u0930\u093f\u0924 \u0915\u0930\u0924\u0940 \u0939\u0948\u0964 \u092f\u0947 \u0938\u0902\u0915\u0947\u0924 \u0915\u094b\u0936\u093f\u0915\u093e\u0913\u0902 \u0915\u0947 \u092a\u094d\u0930\u0938\u093e\u0930, \u0935\u093f\u092d\u0947\u0926\u0928, \u0935\u093f\u0915\u093e\u0938, \u0938\u0942\u091c\u0928 \u092a\u094d\u0930\u0924\u093f\u0915\u094d\u0930\u093f\u092f\u093e\u0913\u0902 \u0914\u0930 \u0915\u094d\u0930\u092e\u093e\u0926\u0947\u0936\u093f\u0924 \u0915\u094b\u0936\u093f\u0915\u093e \u092e\u0943\u0924\u094d\u092f\u0941 \u0915\u094b \u0928\u093f\u092f\u0902\u0924\u094d\u0930\u093f\u0924 \u0915\u0930\u0924\u0947 \u0939\u0948\u0902\u0964 MEK inhibitors \u0915\u094b \u0906\u092e \u0924\u094c\u0930 \u092a\u0930 \u0909\u0928 \u0938\u092d\u0940 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u092e\u093e\u0928\u093e \u091c\u093e\u0924\u093e \u0939\u0948 \u091c\u093f\u0928\u092e\u0947\u0902 <em>BRAF V600E<\/em> \u0909\u0924\u094d\u092a\u0930\u093f\u0935\u0930\u094d\u0924\u0928 \u0928\u0939\u0940\u0902 \u0939\u0948, \u091c\u093f\u0938\u092e\u0947\u0902 \u0935\u0947 \u0930\u094b\u0917\u0940 \u092d\u0940 \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0902 \u091c\u0939\u093e\u0902 \u0915\u093f\u0938\u0940 \u092d\u0940 \u0905\u0928\u0941\u0915\u094d\u0930\u092e\u0923 \u0915\u0947 \u0938\u093e\u0925 \u0915\u094b\u0908 \u0909\u0924\u094d\u092a\u0930\u093f\u0935\u0930\u094d\u0924\u0928 \u0928\u0939\u0940\u0902 \u092a\u093e\u092f\u093e \u091c\u093e\u0924\u093e \u0939\u0948\u0964 \u0906\u092e\u0924\u094c\u0930 \u092a\u0930 \u0909\u092a\u092f\u094b\u0917 \u0915\u093f\u090f \u091c\u093e\u0928\u0947 \u0935\u093e\u0932\u0947 MEK inhibitors \u092e\u0947\u0902 cobimetinib, trametinib, binimetinib \u0914\u0930 selumetinib \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0902\u0964 USA \u092e\u0947\u0902, cobimetinib \u092c\u093f\u0928\u093e <em>BRAF V600E<\/em> \u0935\u093e\u0932\u0947 ECD \u0915\u0947 \u0932\u093f\u090f \u090f\u0915 FDA-\u0905\u0928\u0941\u092e\u094b\u0926\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 \u0939\u0948\u0964     <\/li>\n<li><strong>\u0926\u0941\u0930\u094d\u0932\u092d \u0909\u0924\u094d\u092a\u0930\u093f\u0935\u0930\u094d\u0924\u0928 \u0915\u0947 \u0926\u0941\u0930\u094d\u0932\u092d \u0909\u0926\u093e\u0939\u0930\u0923<\/strong><br \/>\u092c\u0939\u0941\u0924 \u0915\u092e \u0939\u0940, ECD \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u092e\u0947\u0902 \u0905\u0928\u094d\u092f \u0906\u0928\u0941\u0935\u0902\u0936\u093f\u0915 \u0905\u0938\u093e\u092e\u093e\u0928\u094d\u092f\u0924\u093e\u090f\u0902 \u0939\u094b \u0938\u0915\u0924\u0940 \u0939\u0948\u0902 \u0914\u0930 \u0935\u0947 MEK inhibitors \u0915\u0947 \u092a\u094d\u0930\u0924\u093f \u092a\u094d\u0930\u0924\u093f\u0915\u094d\u0930\u093f\u092f\u093e \u0928\u0939\u0940\u0902 \u0915\u0930\u0924\u0947 \u0939\u0948\u0902\u0964 \u0935\u0930\u094d\u0924\u092e\u093e\u0928 \u092e\u0947\u0902, ECD \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u092c\u0939\u0941\u0924 \u091b\u094b\u091f\u0947 \u092a\u094d\u0930\u0924\u093f\u0936\u0924 \u092e\u0947\u0902 \u0928\u093f\u092e\u094d\u0928\u0932\u093f\u0916\u093f\u0924 \u0909\u0924\u094d\u092a\u0930\u093f\u0935\u0930\u094d\u0924\u0928\u094b\u0902 \u0915\u0940 \u0916\u094b\u091c \u0915\u0940 \u0917\u0908 \u0939\u0948, \u091c\u093f\u0928\u092e\u0947\u0902 \u0938\u0942\u091a\u0940\u092c\u0926\u094d\u0927 \u0938\u0902\u092c\u0902\u0927\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 \u0915\u0940 \u0938\u0940\u092e\u093f\u0924 \u0930\u093f\u092a\u094b\u0930\u094d\u091f\u093f\u0902\u0917 \u0939\u0948\u0964 <\/li>\n<\/ul>\n\n<table id=\"tablepress-2\" class=\"tablepress tablepress-id-2\">\n<thead>\n<tr class=\"row-1\">\n\t<th class=\"column-1\"><strong>Discovered Mutation in the ECD Lesion<\/strong><\/th><th class=\"column-2\"><strong>Possible Therapy<\/strong><\/th>\n<\/tr>\n<\/thead>\n<tbody class=\"row-striping row-hover\">\n<tr class=\"row-2\">\n\t<td class=\"column-1\">ALK fusion<\/td><td class=\"column-2\">Crizotinib<\/td>\n<\/tr>\n<tr class=\"row-3\">\n\t<td class=\"column-1\">CSF1R mutation<\/td><td class=\"column-2\">Pexidartinib<\/td>\n<\/tr>\n<tr class=\"row-4\">\n\t<td class=\"column-1\">NTRK gene fusion<\/td><td class=\"column-2\">Larotrectinib<\/td>\n<\/tr>\n<tr class=\"row-5\">\n\t<td class=\"column-1\">NTRK gene fusion<\/td><td class=\"column-2\">Entrectinib<\/td>\n<\/tr>\n<tr class=\"row-6\">\n\t<td class=\"column-1\">PIK3CA mutation<\/td><td class=\"column-2\">Sirolimus<\/td>\n<\/tr>\n<tr class=\"row-7\">\n\t<td class=\"column-1\">RET fusion<\/td><td class=\"column-2\">Selpercatinib<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<!-- #tablepress-2 from cache -->\n<ul>\n<li><strong>\u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u0940 \u0916\u0941\u0930\u093e\u0915<\/strong><strong><br \/><\/strong>\u092f\u0939 \u0927\u094d\u092f\u093e\u0928 \u0926\u093f\u092f\u093e \u091c\u093e\u0928\u093e \u091a\u093e\u0939\u093f\u090f \u0915\u093f \u0905\u0927\u093f\u0915\u093e\u0902\u0936 ECD \u0930\u094b\u0917\u0940 \u0905\u0915\u094d\u0938\u0930 \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 \u0926\u0935\u093e\u0913\u0902 \u0915\u0940 \u0915\u0947\u0935\u0932 \u0915\u092e \u0916\u0941\u0930\u093e\u0915 \u0915\u094b \u0938\u0939\u0928 \u0915\u0930 \u0938\u0915\u0924\u0947 \u0939\u0948\u0902\u0964 \u0907\u0938 \u0915\u093e\u0930\u0923 \u0938\u0947, ECD \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u0928\u093f\u0930\u094d\u0927\u093e\u0930\u093f\u0924 \u0915\u0940 \u0917\u0908 \u0916\u0941\u0930\u093e\u0915 \u0906\u092e \u0924\u094c\u0930 \u092a\u0930 \u0905\u0928\u094d\u092f \u092c\u0940\u092e\u093e\u0930\u093f\u092f\u094b\u0902 \u0915\u0947 \u0909\u092a\u091a\u093e\u0930 \u092e\u0947\u0902 \u0909\u092a\u092f\u094b\u0917 \u0915\u0940 \u091c\u093e\u0928\u0947 \u0935\u093e\u0932\u0940 \u0916\u0941\u0930\u093e\u0915 \u0938\u0947 \u0915\u092e \u0939\u094b\u0924\u0940 \u0939\u0948\u0964 \u0935\u0930\u094d\u0924\u092e\u093e\u0928 \u092e\u0947\u0902, \u0939\u093e\u0932\u093e\u0902\u0915\u093f \u0907\u0928 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u094b \u0905\u0915\u094d\u0938\u0930 \u0905\u0928\u093f\u0936\u094d\u091a\u093f\u0924 \u0915\u093e\u0932 \u0924\u0915 \u091c\u093e\u0930\u0940 \u0930\u0916\u093e \u091c\u093e\u0928\u093e \u091a\u093e\u0939\u093f\u090f, \u090f\u0915 \u092c\u093e\u0930 \u091c\u092c \u0930\u094b\u0917\u0940 \u0915\u0940 \u092c\u0940\u092e\u093e\u0930\u0940 \u0909\u092a\u091a\u093e\u0930 \u092a\u0930 \u092a\u0942\u0930\u0940 \u0924\u0930\u0939 \u0938\u0947 \u0938\u094d\u0925\u093f\u0930 \u0939\u094b \u091c\u093e\u0924\u0940 \u0939\u0948 \u0924\u094b \u0905\u0915\u094d\u0938\u0930 \u0916\u0941\u0930\u093e\u0915 \u092e\u0947\u0902 \u0914\u0930 \u0915\u092e\u0940 \u0938\u0902\u092d\u0935 \u0939\u094b\u0924\u0940 \u0939\u0948\u0964 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u094b \u0905\u092a\u0928\u0940 \u0909\u092a\u091a\u093e\u0930 \u0916\u0941\u0930\u093e\u0915 \u092e\u0947\u0902 \u0915\u093f\u0938\u0940 \u092d\u0940 \u092a\u094d\u0930\u0938\u094d\u0924\u093e\u0935\u093f\u0924 \u092a\u0930\u093f\u0935\u0930\u094d\u0924\u0928 \u0915\u0947 \u092c\u093e\u0930\u0947 \u092e\u0947\u0902 \u092a\u0930\u093f\u0935\u0930\u094d\u0924\u0928 \u0915\u0930\u0928\u0947 \u0938\u0947 \u092a\u0939\u0932\u0947 \u0939\u092e\u0947\u0936\u093e \u0905\u092a\u0928\u0947 \u0921\u0949\u0915\u094d\u091f\u0930 \u0938\u0947 \u091a\u0930\u094d\u091a\u093e \u0915\u0930\u0928\u0940 \u091a\u093e\u0939\u093f\u090f\u0964   <\/li>\n<li><strong>\u0909\u092a\u091a\u093e\u0930 \u092a\u094d\u0930\u092a\u0924\u094d\u0930<\/strong><br \/> \u0905\u0927\u093f\u0915\u093e\u0902\u0936 \u092e\u093e\u092e\u0932\u094b\u0902 \u092e\u0947\u0902, \u0938\u092d\u0940 \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 \u0917\u094b\u0932\u0940 \u0915\u0947 \u0930\u0942\u092a \u092e\u0947\u0902, \u0926\u093f\u0928 \u092e\u0947\u0902 \u090f\u0915 \u092f\u093e \u0926\u094b \u092c\u093e\u0930 \u0926\u093f\u090f \u091c\u093e\u0924\u0947 \u0939\u0948\u0902\u0964<\/li>\n<li><strong>\u0926\u0941\u0937\u094d\u092a\u094d\u0930\u092d\u093e\u0935<\/strong><br \/> \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u0947 \u0926\u0941\u0937\u094d\u092a\u094d\u0930\u092d\u093e\u0935\u094b\u0902 \u0915\u094b \u0930\u094b\u0917\u0940 \u0914\u0930 \u0909\u0928\u0915\u0940 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u093e \u091f\u0940\u092e \u0915\u0947 \u092c\u0940\u091a \u0938\u093e\u091d\u0947\u0926\u093e\u0930\u0940 \u0915\u0947 \u092e\u093e\u0927\u094d\u092f\u092e \u0938\u0947 \u092a\u094d\u0930\u092c\u0902\u0927\u093f\u0924 \u0915\u093f\u092f\u093e \u091c\u093e\u0928\u093e \u091a\u093e\u0939\u093f\u090f\u0964 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u094b \u0939\u092e\u0947\u0936\u093e \u0915\u093f\u0938\u0940 \u092d\u0940 \u0909\u092a\u091a\u093e\u0930 \u0915\u0940 \u0936\u0941\u0930\u0941\u0906\u0924 \u0915\u0930\u0924\u0947 \u0938\u092e\u092f \u0938\u0902\u092d\u093e\u0935\u093f\u0924 \u0926\u0941\u0937\u094d\u092a\u094d\u0930\u092d\u093e\u0935\u094b\u0902 \u0915\u0947 \u092c\u093e\u0930\u0947 \u092e\u0947\u0902 \u0905\u092a\u0928\u0940 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u093e \u091f\u0940\u092e \u0938\u0947 \u092a\u0942\u091b\u0928\u093e \u091a\u093e\u0939\u093f\u090f\u0964 BRAF \u0905\u0935\u0930\u094b\u0927\u0915\u094b\u0902 \u0915\u0947 \u0938\u093e\u092e\u093e\u0928\u094d\u092f \u0926\u0941\u0937\u094d\u092a\u094d\u0930\u092d\u093e\u0935\u094b\u0902 \u092e\u0947\u0902 \u0926\u093e\u0928\u0947, \u091c\u094b\u0921\u093c\u094b\u0902 \u092e\u0947\u0902 \u0926\u0930\u094d\u0926 \u0914\u0930 \u0924\u094d\u0935\u091a\u093e \u0915\u0940 \u0938\u0942\u0930\u094d\u092f \u0915\u0947 \u092a\u094d\u0930\u0924\u093f \u0938\u0902\u0935\u0947\u0926\u0928\u0936\u0940\u0932\u0924\u093e \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0964 MEK \u0905\u0935\u0930\u094b\u0927\u0915\u094b\u0902 \u0915\u0947 \u0938\u093e\u092e\u093e\u0928\u094d\u092f \u0926\u0941\u0937\u094d\u092a\u094d\u0930\u092d\u093e\u0935\u094b\u0902 \u092e\u0947\u0902 \u0926\u093e\u0928\u0947, \u0926\u0938\u094d\u0924 \u0914\u0930 \u092a\u0948\u0930\u094b\u0902 \u0915\u0940 \u0938\u0942\u091c\u0928 \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0902\u0964 BRAF \u0905\u0935\u0930\u094b\u0927\u0915\u094b\u0902 \u0915\u0947 \u0926\u0941\u0930\u094d\u0932\u092d \u0926\u0941\u0937\u094d\u092a\u094d\u0930\u092d\u093e\u0935\u094b\u0902 \u092e\u0947\u0902 \u0924\u094d\u0935\u091a\u093e \u0915\u0948\u0902\u0938\u0930 \u092f\u093e \u0939\u0943\u0926\u092f \u0924\u093e\u0932 \u0915\u0940 \u0938\u092e\u0938\u094d\u092f\u093e\u090f\u0902 \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0902, \u0914\u0930 MEK \u0905\u0935\u0930\u094b\u0927\u0915\u094b\u0902 \u0915\u0947 \u0926\u0941\u0937\u094d\u092a\u094d\u0930\u092d\u093e\u0935\u094b\u0902 \u092e\u0947\u0902 \u0926\u0943\u0937\u094d\u091f\u093f \u0938\u0902\u092c\u0902\u0927\u0940 \u0917\u0921\u093c\u092c\u0921\u093c\u0940 \u0914\u0930 \u0939\u0943\u0926\u092f \u0917\u0924\u093f \u0930\u0941\u0915\u0928\u093e \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0902\u0964    <\/li>\n<li><strong>\u0909\u092a\u091a\u093e\u0930 \u0932\u093e\u0917\u0924<\/strong><br \/> \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 \u0915\u0940 \u0932\u093e\u0917\u0924 \u0915\u092d\u0940-\u0915\u092d\u0940 \u092c\u0939\u0941\u0924 \u0905\u0927\u093f\u0915 \u0939\u094b \u0938\u0915\u0924\u0940 \u0939\u0948\u0964 \u0915\u0941\u091b \u0926\u0947\u0936\u094b\u0902 \u092e\u0947\u0902, \u092c\u0940\u092e\u093e \u0914\u0930 \u0938\u0930\u0915\u093e\u0930\u0940 \u092d\u0941\u0917\u0924\u093e\u0928\u0915\u0930\u094d\u0924\u093e \u0909\u092a\u091a\u093e\u0930 \u0915\u0940 \u0932\u093e\u0917\u0924 \u0915\u093e \u0905\u0927\u093f\u0915\u093e\u0902\u0936 \u0939\u093f\u0938\u094d\u0938\u093e \u0935\u0939\u0928 \u0915\u0930\u0947\u0902\u0917\u0947\u0964 \u0915\u0941\u091b \u0938\u094d\u0925\u093e\u0928\u094b\u0902 \u092a\u0930, \u0910\u0938\u0947 \u0938\u0902\u0917\u0920\u0928 \u0939\u094b \u0938\u0915\u0924\u0947 \u0939\u0948\u0902 \u091c\u094b \u0930\u094b\u0917\u0940 \u0915\u0940 \u0906\u092f \u0915\u0947 \u0906\u0927\u093e\u0930 \u092a\u0930 \u0909\u092a\u091a\u093e\u0930 \u0915\u0940 \u0936\u0947\u0937 \u0932\u093e\u0917\u0924 \u092e\u0947\u0902 \u092e\u0926\u0926 \u0915\u0930 \u0938\u0915\u0924\u0947 \u0939\u0948\u0902\u0964 \u092b\u093f\u0930 \u092d\u0940, \u0905\u0928\u094d\u092f \u0938\u094d\u0925\u093e\u0928\u094b\u0902 \u092a\u0930, \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0924\u0915 \u092a\u0939\u0941\u0901\u091a \u092c\u0947\u0939\u0926 \u0938\u0940\u092e\u093f\u0924 \u0939\u0948\u0964 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u094b \u0907\u0928 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u0940 \u0932\u093e\u0917\u0924\u094b\u0902 \u0915\u0947 \u092c\u093e\u0930\u0947 \u092e\u0947\u0902 \u0905\u092a\u0928\u0940 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u093e \u091f\u0940\u092e \u0938\u0947 \u092c\u093e\u0924 \u0915\u0930\u0928\u0940 \u091a\u093e\u0939\u093f\u090f \u0914\u0930 \u092d\u0941\u0917\u0924\u093e\u0928 \u0935\u093f\u0915\u0932\u094d\u092a\u094b\u0902 \u092a\u0930 \u091a\u0930\u094d\u091a\u093e \u0915\u0930\u0928\u0940 \u091a\u093e\u0939\u093f\u090f\u0964 ECDGA \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0914\u0930 \u0909\u0928\u0915\u0940 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u093e \u091f\u0940\u092e\u094b\u0902 \u0915\u0947 \u0938\u093e\u0925 \u0915\u093e\u092e \u0915\u0930\u0928\u0947 \u0915\u0947 \u0932\u093f\u090f \u0909\u092a\u0932\u092c\u094d\u0927 \u0939\u0948 \u0924\u093e\u0915\u093f \u091c\u0939\u093e\u0901 \u0938\u0902\u092d\u0935 \u0939\u094b, \u092d\u0941\u0917\u0924\u093e\u0928 \u0935\u093f\u0915\u0932\u094d\u092a\u094b\u0902 \u0915\u0940 \u0916\u094b\u091c \u0915\u0930\u0928\u0947 \u092e\u0947\u0902 \u092e\u0926\u0926 \u092e\u093f\u0932 \u0938\u0915\u0947\u0964     <\/li>\n<\/ul>\n<p><strong>\u0915\u0940\u092e\u094b\u0925\u0947\u0930\u092a\u0940<\/strong><\/p>\n<p>\u0915\u0940\u092e\u094b\u0925\u0947\u0930\u0947\u092a\u0940 \u092e\u0947\u0902 \u0910\u0938\u0940 \u0926\u0935\u093e\u0913\u0902 \u0915\u093e \u0907\u0938\u094d\u0924\u0947\u092e\u093e\u0932 \u0915\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0939\u0948 \u091c\u094b \u0915\u0948\u0902\u0938\u0930 \u0915\u094b\u0936\u093f\u0915\u093e\u0913\u0902 \u092f\u093e \u0905\u0928\u094d\u092f \u0924\u0947\u091c\u093c\u0940 \u0938\u0947 \u0935\u093f\u092d\u093e\u091c\u093f\u0924 \u0939\u094b\u0928\u0947 \u0935\u093e\u0932\u0940 \u0915\u094b\u0936\u093f\u0915\u093e\u0913\u0902 \u0915\u094b \u0928\u0937\u094d\u091f \u0915\u0930 \u0926\u0947\u0924\u0940 \u0939\u0948\u0902\u0964 ECD \u0915\u0947 \u0909\u092a\u091a\u093e\u0930 \u092e\u0947\u0902 \u0915\u0908 \u0915\u0940\u092e\u094b\u0925\u0947\u0930\u0947\u092a\u0940 \u092a\u0926\u094d\u0927\u0924\u093f\u092f\u094b\u0902 \u0915\u093e \u0907\u0938\u094d\u0924\u0947\u092e\u093e\u0932 \u0915\u093f\u092f\u093e \u0917\u092f\u093e \u0939\u0948\u0964 \u0907\u0928\u092e\u0947\u0902 \u0915\u094d\u0932\u0948\u0921\u094d\u0930\u093f\u092c\u093e\u0907\u0928 \u0914\u0930 \u092e\u0947\u0925\u094b\u091f\u094d\u0930\u0947\u0915\u094d\u0938\u0947\u091f \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0902\u0964 \u091b\u094b\u091f\u0947 \u0905\u0927\u094d\u092f\u092f\u0928\u094b\u0902 \u0938\u0947 \u092a\u0924\u093e \u091a\u0932\u093e \u0939\u0948 \u0915\u093f \u0915\u0941\u091b \u092e\u0930\u0940\u091c\u093c \u0915\u0940\u092e\u094b\u0925\u0947\u0930\u0947\u092a\u0940 \u0915\u0947 \u092a\u094d\u0930\u0924\u093f \u0905\u091a\u094d\u091b\u0940 \u092a\u094d\u0930\u0924\u093f\u0915\u094d\u0930\u093f\u092f\u093e \u0926\u0947\u0924\u0947 \u0939\u0948\u0902, \u0939\u093e\u0932\u093e\u0901\u0915\u093f \u092a\u094d\u0930\u0924\u093f\u0915\u094d\u0930\u093f\u092f\u093e \u0926\u0930 \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u0940 \u0924\u0941\u0932\u0928\u093e \u092e\u0947\u0902 \u092c\u0939\u0941\u0924 \u0915\u092e \u0939\u0948\u0964 \u0907\u0928 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u093e \u090f\u0915 \u092b\u093c\u093e\u092f\u0926\u093e \u092f\u0939 \u0939\u0948 \u0915\u093f \u0915\u0941\u091b \u092e\u0930\u0940\u091c\u093c\u094b\u0902 \u0928\u0947 \u0938\u0940\u092e\u093f\u0924 \u0905\u0935\u0927\u093f \u0915\u0947 \u0909\u092a\u091a\u093e\u0930 \u0915\u0947 \u0938\u093e\u0925 \u0932\u0902\u092c\u0947 \u0938\u092e\u092f \u0924\u0915 \u092a\u094d\u0930\u0924\u093f\u0915\u094d\u0930\u093f\u092f\u093e \u0915\u093e \u0905\u0928\u0941\u092d\u0935 \u0915\u093f\u092f\u093e \u0939\u0948\u0964    <\/p>\n<ul>\n<li><strong>\u0915\u094d\u0932\u0948\u0921\u094d\u0930\u0940\u092c\u093e\u0908\u0928<\/strong><br \/> \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 \u0909\u092a\u0932\u092c\u094d\u0927 \u0939\u094b\u0928\u0947 \u0938\u0947 \u092a\u0939\u0932\u0947, \u0915\u094d\u0932\u0948\u0921\u094d\u0930\u093f\u092c\u093e\u0907\u0928 \u0915\u093e \u0909\u092a\u092f\u094b\u0917 ECD \u0909\u092a\u091a\u093e\u0930 \u0915\u0947 \u0930\u0942\u092a \u092e\u0947\u0902 \u0915\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0925\u093e \u0914\u0930 \u0907\u0938\u0915\u093e \u0905\u0927\u094d\u092f\u092f\u0928 \u0915\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0925\u093e\u0964 \u0907\u0938\u0928\u0947 ECD \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u092e\u0927\u094d\u092f\u092e \u092a\u094d\u0930\u092d\u093e\u0935\u0915\u093e\u0930\u093f\u0924\u093e \u0926\u093f\u0916\u093e\u0908\u0964 \u0906\u092e \u0924\u094c\u0930 \u092a\u0930, \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u094b \u0905\u0902\u0924\u0903\u0936\u093f\u0930\u093e \u0907\u0902\u091c\u0947\u0915\u094d\u0936\u0928 \u0915\u0947 \u092e\u093e\u0927\u094d\u092f\u092e \u0938\u0947 2-3 \u092e\u0939\u0940\u0928\u0947 \u0915\u0947 \u0932\u093f\u090f, \u0939\u0930 28 \u0926\u093f\u0928 \u092e\u0947\u0902 \u092a\u093e\u0902\u091a \u0926\u093f\u0928\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u0915\u094d\u0932\u0948\u0921\u094d\u0930\u093f\u092c\u093e\u0907\u0928 \u0926\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0925\u093e\u0964  <\/li>\n<li><strong>methotrexate<\/strong><br \/> ECD \u0915\u0947 \u0909\u092a\u091a\u093e\u0930 \u0915\u0947 \u0930\u0942\u092a \u092e\u0947\u0902 \u092e\u0947\u0925\u094b\u091f\u094d\u0930\u0947\u0915\u094d\u0938\u0947\u091f \u0915\u0947 \u0909\u092a\u092f\u094b\u0917 \u0928\u0947 \u0915\u092e \u092a\u094d\u0930\u0924\u093f\u0915\u094d\u0930\u093f\u092f\u093e \u0926\u0930 \u0926\u093f\u0916\u093e\u0908 \u0939\u0948\u0964 \u0939\u093e\u0932\u093e\u0901\u0915\u093f, \u092f\u0939 \u0909\u092a\u091a\u093e\u0930 \u0906\u092e \u0924\u094c\u0930 \u092a\u0930 \u0905\u091a\u094d\u091b\u0940 \u0924\u0930\u0939 \u0938\u0947 \u0938\u0939\u0928 \u0915\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0939\u0948 \u0914\u0930 \u0907\u0938 \u092a\u094d\u0930\u0915\u093e\u0930 \u0909\u0928 \u0932\u094b\u0917\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u092b\u093e\u092f\u0926\u0947\u092e\u0902\u0926 \u0939\u094b \u0938\u0915\u0924\u093e \u0939\u0948 \u091c\u093f\u0928\u0915\u0947 \u0932\u093f\u090f \u092f\u0939 \u0915\u093e\u092e \u0915\u0930\u0924\u093e \u0939\u0948\u0964 \u092e\u0947\u0925\u094b\u091f\u094d\u0930\u0947\u0915\u094d\u0938\u0947\u091f \u0915\u094b \u091c\u0932\u0938\u0947\u0915, \u0907\u0902\u091c\u0947\u0915\u094d\u0936\u0928 \u092f\u093e \u091f\u0948\u092c\u0932\u0947\u091f \u0915\u0947 \u0930\u0942\u092a \u092e\u0947\u0902 \u0926\u093f\u092f\u093e \u091c\u093e \u0938\u0915\u0924\u093e \u0939\u0948\u0964 ECD \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f, \u0907\u0938\u0947 \u0906\u092e \u0924\u094c\u0930 \u092a\u0930 \u092e\u093e\u0902\u0938\u092a\u0947\u0936\u093f\u092f\u094b\u0902 \u092e\u0947\u0902 \u0938\u093e\u092a\u094d\u0924\u093e\u0939\u093f\u0915 \u0907\u0902\u091c\u0947\u0915\u094d\u0936\u0928 \u0915\u0947 \u0930\u0942\u092a \u092e\u0947\u0902 \u0926\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0939\u0948\u0964   <\/li>\n<\/ul>\n<p><strong>immunotherapy<\/strong><br \/> \u092a\u094d\u0930\u0924\u093f\u0930\u0915\u094d\u0937\u093e-\u0938\u0902\u0936\u094b\u0927\u093f\u0924 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u093e, ECD \u0918\u093e\u0935\u094b\u0902 \u0915\u094b \u0938\u093f\u0915\u094b\u0921\u093c\u0928\u0947 \u0915\u0947 \u0932\u093f\u090f \u092a\u094d\u0930\u0924\u093f\u0930\u0915\u094d\u0937\u093e \u092a\u094d\u0930\u0923\u093e\u0932\u0940 \u0915\u094b \u0909\u0924\u094d\u0924\u0947\u091c\u093f\u0924 \u092f\u093e \u0926\u092c\u093e\u0915\u0930 \u0915\u093e\u092e \u0915\u0930 \u0938\u0915\u0924\u0940 \u0939\u0948\u0964<\/p>\n<ul>\n<li><strong>Interferon<\/strong><br \/>ECD \u0915\u0947 \u0932\u093f\u090f \u0916\u094b\u091c\u093e \u0917\u092f\u093e \u092a\u0939\u0932\u093e \u0909\u092a\u091a\u093e\u0930 interferon \u0925\u093e, \u091c\u094b immunotherapy \u0915\u093e \u090f\u0915 \u0930\u0942\u092a \u0939\u0948\u0964 \u091c\u0939\u093e\u0902 \u0909\u092a\u0932\u092c\u094d\u0927 \u0939\u094b, pegylated interferon alpha \u092a\u0938\u0902\u0926\u0940\u0926\u093e interferon \u0909\u092a\u091a\u093e\u0930 \u0939\u0948 \u0915\u094d\u092f\u094b\u0902\u0915\u093f \u0907\u0938\u0947 \u092c\u0947\u0939\u0924\u0930 \u0938\u0939\u0928\u0936\u0940\u0932\u0924\u093e \u092a\u094d\u0930\u094b\u092b\u093c\u093e\u0907\u0932 \u0915\u0947 \u0938\u093e\u0925 \u0915\u092e \u092c\u093e\u0930 \u0926\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0939\u0948\u0964 \u0939\u093e\u0932\u093e\u0902\u0915\u093f, \u092f\u0939 \u092b\u0949\u0930\u094d\u092e\u0942\u0932\u0947\u0936\u0928 \u0938\u092d\u0940 \u0926\u0947\u0936\u094b\u0902 \u092e\u0947\u0902 \u0909\u092a\u0932\u092c\u094d\u0927 \u0928\u0939\u0940\u0902 \u0939\u0948\u0964 Interferon alpha-2a \u0915\u093e \u0909\u092a\u092f\u094b\u0917 ECD \u0915\u0947 \u0909\u092a\u091a\u093e\u0930 \u092e\u0947\u0902 \u0915\u093f\u092f\u093e \u0917\u092f\u093e \u0939\u0948 \u0914\u0930 \u0907\u0938\u0947 \u0905\u0927\u093f\u0915 \u092c\u093e\u0930 \u0932\u0947\u0928\u0947 \u0915\u0940 \u0906\u0935\u0936\u094d\u092f\u0915\u0924\u093e \u0939\u094b\u0924\u0940 \u0939\u0948\u0964 Interferon \u0915\u094b \u0906\u092e \u0924\u094c\u0930 \u092a\u0930 \u0918\u0930 \u092a\u0930 \u0906\u092a\u0915\u0940 \u0924\u094d\u0935\u091a\u093e \u0915\u0947 \u0928\u0940\u091a\u0947 \u092f\u093e \u092e\u093e\u0902\u0938\u092a\u0947\u0936\u0940 \u092e\u0947\u0902 \u090f\u0915 \u0936\u0949\u091f \u0915\u0947 \u092e\u093e\u0927\u094d\u092f\u092e \u0938\u0947 \u0926\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0939\u0948\u0964 \u092f\u0939 \u0909\u092a\u091a\u093e\u0930 \u0905\u0915\u094d\u0938\u0930 \u0905\u0928\u093f\u0936\u094d\u091a\u093f\u0924 \u0915\u093e\u0932 \u0924\u0915 \u091c\u093e\u0930\u0940 \u0930\u0916\u093e \u091c\u093e\u0928\u093e \u091a\u093e\u0939\u093f\u090f\u0964 \u0939\u093e\u0932\u093e\u0902\u0915\u093f \u0915\u0941\u091b \u0930\u094b\u0917\u0940 interferon \u0909\u092a\u091a\u093e\u0930 \u0915\u094b \u0906\u0938\u093e\u0928\u0940 \u0938\u0947 \u0938\u0939\u0928 \u0915\u0930 \u0938\u0915\u0924\u0947 \u0939\u0948\u0902, \u0915\u0908 \u0930\u094b\u0917\u0940 \u0909\u092a\u091a\u093e\u0930 \u0915\u0947 \u0905\u0928\u0941\u0915\u0942\u0932 \u0939\u094b\u0928\u0947 \u092a\u0930 \u092b\u094d\u0932\u0942 \u091c\u0948\u0938\u0940 \u092d\u093e\u0935\u0928\u093e\u0913\u0902 \u0915\u0940 \u0930\u093f\u092a\u094b\u0930\u094d\u091f \u0915\u0930\u0924\u0947 \u0939\u0948\u0902\u0964 \u092f\u0939 \u0909\u092a\u091a\u093e\u0930 ECD \u0915\u0940 \u092a\u094d\u0930\u0917\u0924\u093f \u0915\u094b \u0927\u0940\u092e\u093e \u0915\u0930\u0928\u0947 \u0915\u0947 \u0932\u093f\u090f \u092a\u093e\u092f\u093e \u0917\u092f\u093e \u0939\u0948\u0964 Interferon \u0915\u093e \u090f\u0915 \u0932\u0902\u092c\u0947 \u0938\u092e\u092f \u0924\u0915 \u0915\u093e\u092e \u0915\u0930\u0928\u0947 \u0935\u093e\u0932\u093e \u0938\u0902\u0938\u094d\u0915\u0930\u0923 \u091c\u093f\u0938\u092e\u0947\u0902 \u0915\u0947\u0935\u0932 \u0938\u092a\u094d\u0924\u093e\u0939 \u092e\u0947\u0902 \u090f\u0915 \u092c\u093e\u0930 \u0907\u0902\u091c\u0947\u0915\u094d\u0936\u0928 \u0915\u0940 \u0906\u0935\u0936\u094d\u092f\u0915\u0924\u093e \u0939\u094b\u0924\u0940 \u0939\u0948, peginterferon, \u092d\u0940 \u0909\u092a\u0932\u092c\u094d\u0927 \u0939\u0948\u0964        <\/li>\n<li><strong>\u0938\u093f\u0930\u094b\u0932\u093f\u092e\u0938 \u0914\u0930 \u090f\u0935\u0930\u094b\u0932\u093f\u092e\u0938<\/strong><br \/> \u090f\u0915 \u091b\u094b\u091f\u0947 \u0938\u0947 \u0905\u0927\u094d\u092f\u092f\u0928 \u092e\u0947\u0902 \u092a\u093e\u092f\u093e \u0917\u092f\u093e \u0915\u093f \u0938\u093f\u0930\u094b\u0932\u093f\u092e\u0938 \u0914\u0930 \u090f\u0935\u0930\u094b\u0932\u093f\u092e\u0938, \u0907\u092e\u094d\u092f\u0942\u0928\u094b\u0938\u092a\u094d\u0930\u0947\u0938\u093f\u0935 \u0925\u0947\u0930\u0947\u092a\u0940 \u0915\u0947 \u0930\u0942\u092a \u0939\u0948\u0902, \u091c\u094b \u0932\u0917\u092d\u0917 60% ECD \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u092e\u0927\u094d\u092f\u092e \u092a\u094d\u0930\u092d\u093e\u0935\u0915\u093e\u0930\u093f\u0924\u093e \u0930\u0916\u0924\u0947 \u0939\u0948\u0902\u0964 \u092f\u0939 \u0909\u092a\u091a\u093e\u0930 \u0906\u092e \u0924\u094c\u0930 \u092a\u0930 \u0926\u093f\u0928 \u092e\u0947\u0902 \u090f\u0915 \u092c\u093e\u0930 \u091f\u0948\u092c\u0932\u0947\u091f \u092f\u093e \u0924\u0930\u0932 \u0930\u0942\u092a \u092e\u0947\u0902 \u0926\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0939\u0948\u0964 <\/li>\n<li><strong>\u091c\u0948\u0935\u093f\u0915 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u093e<\/strong><br \/> \u091c\u0948\u0935\u093f\u0915 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u093e \u090f\u0915 \u092a\u094d\u0930\u0915\u093e\u0930 \u0915\u093e \u0909\u092a\u091a\u093e\u0930 \u0939\u0948 \u091c\u094b ECD \u0915\u094b\u0936\u093f\u0915\u093e\u0913\u0902 \u0926\u094d\u0935\u093e\u0930\u093e \u0909\u0924\u094d\u092a\u093e\u0926\u093f\u0924 \u0905\u0938\u093e\u092e\u093e\u0928\u094d\u092f \u0930\u0938\u093e\u092f\u0928\u094b\u0902 (\u0938\u093e\u0907\u091f\u094b\u0915\u093e\u0907\u0928\u094d\u0938) \u0915\u094b \u0926\u092c\u093e \u0926\u0947\u0924\u093e \u0939\u0948, \u091c\u093f\u0938\u0938\u0947 \u0938\u0942\u091c\u0928 \u092a\u0948\u0926\u093e \u0939\u094b\u0924\u0940 \u0939\u0948, \u091c\u093f\u0938\u0915\u0947 \u092a\u0930\u093f\u0923\u093e\u092e\u0938\u094d\u0935\u0930\u0942\u092a \u0918\u093e\u0935 \u0938\u093f\u0915\u0941\u0921\u093c \u091c\u093e\u0924\u0947 \u0939\u0948\u0902\u0964<\/li>\n<\/ul>\n<ul>\n<li><strong>Anakinra<\/strong><br \/>\u091b\u094b\u091f\u0947 \u0905\u0927\u094d\u092f\u092f\u0928\u094b\u0902 \u0938\u0947 \u092a\u0924\u093e \u091a\u0932\u093e \u0939\u0948 \u0915\u093f \u0915\u0941\u091b \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0928\u0947 ECD \u0915\u0947 \u0932\u093f\u090f \u0909\u092a\u091a\u093e\u0930 \u0935\u093f\u0915\u0932\u094d\u092a \u0915\u0947 \u0930\u0942\u092a \u092e\u0947\u0902 Anakinra \u0915\u0947 \u092a\u094d\u0930\u0924\u093f \u092a\u094d\u0930\u0924\u093f\u0915\u094d\u0930\u093f\u092f\u093e \u0926\u0940 \u0939\u0948\u0964 Anakinra \u0915\u094b \u0906\u092e \u0924\u094c\u0930 \u092a\u0930 \u0924\u094d\u0935\u091a\u093e \u0915\u0947 \u0928\u0940\u091a\u0947 \u090f\u0915 \u0907\u0902\u091c\u0947\u0915\u094d\u0936\u0928 \u0915\u0947 \u0930\u0942\u092a \u092e\u0947\u0902 \u0926\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0939\u0948\u0964 ECD \u0915\u0947 \u0932\u093f\u090f \u090f\u0915 \u0938\u094d\u091f\u0948\u0902\u0921-\u0905\u0932\u094b\u0928 \u0909\u092a\u091a\u093e\u0930 \u0915\u0947 \u0930\u0942\u092a \u092e\u0947\u0902 anakinra \u0915\u093e \u0905\u0927\u094d\u092f\u092f\u0928 \u0938\u0940\u092e\u093f\u0924 \u0930\u0939\u093e \u0939\u0948 \u0932\u0947\u0915\u093f\u0928 \u092a\u094d\u0930\u091a\u0932\u093f\u0924 \u092a\u094d\u0930\u0923\u093e\u0932\u0940\u0917\u0924 <a href=\"https:\/\/www.erdheim-chester.org\/hi\/%e0%a4%b2%e0%a4%95%e0%a5%8d%e0%a4%b7%e0%a4%a3\/\">\u0932\u0915\u094d\u0937\u0923\u094b\u0902<\/a> \u0935\u093e\u0932\u0947 \u0909\u0928 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u0938\u0939\u093e\u092f\u0915 \u0939\u094b \u0938\u0915\u0924\u093e \u0939\u0948\u0964 Anakinra \u0915\u093e \u0909\u092a\u092f\u094b\u0917 \u0932\u0915\u094d\u0937\u093f\u0924 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u0940 \u0938\u0939\u0928\u0936\u0940\u0932\u0924\u093e \u092e\u0947\u0902 \u0938\u0941\u0927\u093e\u0930 \u0915\u0947 \u0932\u093f\u090f \u092d\u0940 \u0915\u093f\u092f\u093e \u0917\u092f\u093e \u0939\u0948\u0964   <\/li>\n<li><strong>\u0905\u0928\u094d\u092f \u091c\u0948\u0935\u093f\u0915 \u0909\u092a\u091a\u093e\u0930<\/strong><br \/> \u0915\u092e \u0907\u0938\u094d\u0924\u0947\u092e\u093e\u0932 \u0915\u093f\u092f\u0947 \u091c\u093e\u0928\u0947 \u0935\u093e\u0932\u0947 \u091c\u0948\u0935\u093f\u0915 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u092e\u0947\u0902 \u0915\u0948\u0928\u093e\u0915\u093f\u0928\u0941\u092e\u093e\u092c, \u091f\u094b\u0938\u0940\u0932\u093f\u091c\u093c\u0941\u092e\u0948\u092c \u0914\u0930 \u0907\u0928\u094d\u092b\u094d\u0932\u093f\u0915\u094d\u0938\u093f\u092e\u0948\u092c \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0902\u0964<\/li>\n<\/ul>\n<p><strong>\u0915\u094d\u0932\u093f\u0928\u093f\u0915\u0932 \u092a\u0930\u0940\u0915\u094d\u0937\u0923<\/strong><\/p>\n<p>\u0907\u0938 \u0930\u094b\u0917 \u0915\u0940 \u0926\u0941\u0930\u094d\u0932\u092d\u0924\u093e \u0915\u0947 \u0915\u093e\u0930\u0923, \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u0940 \u092a\u094d\u0930\u092d\u093e\u0935\u0936\u0940\u0932\u0924\u093e \u0915\u093e \u0906\u0915\u0932\u0928 \u0915\u0930\u0928\u0947 \u0915\u0947 \u0932\u093f\u090f \u0910\u0924\u093f\u0939\u093e\u0938\u093f\u0915 \u0930\u0942\u092a \u0938\u0947 <a href=\"https:\/\/www.erdheim-chester.org\/hi\/%e0%a4%85%e0%a4%a7%e0%a5%8d%e0%a4%af%e0%a4%af%e0%a4%a8-%e0%a4%94%e0%a4%b0-%e0%a4%aa%e0%a4%b0%e0%a5%80%e0%a4%95%e0%a5%8d%e0%a4%b7%e0%a4%a3\/\">\u0928\u0948\u0926\u093e\u0928\u093f\u0915 \u200b\u200b\u092a\u0930\u0940\u0915\u094d\u0937\u0923<\/a> \u0928\u0939\u0940\u0902 \u0915\u093f\u090f \u0917\u090f \u0925\u0947\u0964 \u092a\u094d\u0930\u093e\u0930\u0902\u092d\u093f\u0915 \u092a\u094d\u0930\u0932\u0947\u0916\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 \u092c\u0939\u0941\u0924 \u091b\u094b\u091f\u0947 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u0938\u092e\u0942\u0939, \u0915\u092d\u0940-\u0915\u092d\u0940 \u0938\u093f\u0930\u094d\u092b\u093c \u090f\u0915 \u0930\u094b\u0917\u0940 \u0915\u0947 \u0938\u093e\u0925 \u0915\u093f\u090f \u0917\u090f \u0915\u0947\u0938 \u0905\u0927\u094d\u092f\u092f\u0928\u094b\u0902 \u092a\u0930 \u0906\u0927\u093e\u0930\u093f\u0924 \u0925\u0947\u0964 \u0939\u093e\u0932\u093e\u0901\u0915\u093f, \u092f\u0939 \u092c\u0926\u0932 \u0930\u0939\u093e \u0939\u0948\u0964 \u0906\u091c \u0915\u0941\u091b \u0926\u0947\u0936\u094b\u0902 \u092e\u0947\u0902 ECD \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u0915\u0908 \u0905\u0927\u094d\u092f\u092f\u0928 \u0914\u0930 \u0928\u0948\u0926\u093e\u0928\u093f\u0915 \u200b\u200b\u092a\u0930\u0940\u0915\u094d\u0937\u0923 \u0916\u0941\u0932\u0947 \u0939\u0948\u0902\u0964 \u091c\u092c ECD \u0930\u094b\u0917\u0940 \u0928\u0948\u0926\u093e\u0928\u093f\u0915 \u200b\u200b\u092a\u0930\u0940\u0915\u094d\u0937\u0923 \u092e\u0947\u0902 \u0928\u093e\u092e\u093e\u0902\u0915\u0928 \u0915\u0930\u093e\u0924\u0947 \u0939\u0948\u0902, \u0924\u094b \u0935\u0947 ECD \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u0947 \u0932\u093f\u090f \u0909\u092a\u0932\u092c\u094d\u0927 \u0915\u0941\u091b \u0928\u0935\u0940\u0928\u0924\u092e \u0914\u0930 \u0938\u0930\u094d\u0935\u094b\u0924\u094d\u0924\u092e \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0924\u0915 \u092a\u0939\u0941\u0901\u091a \u092a\u094d\u0930\u093e\u092a\u094d\u0924 \u0915\u0930 \u0938\u0915\u0924\u0947 \u0939\u0948\u0902\u0964 \u0938\u092d\u0940 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u094b \u0905\u092a\u0928\u0947 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u0915\u0940\u092f \u0926\u0932 \u0938\u0947 \u0907\u0938 \u092c\u093e\u0930\u0947 \u092e\u0947\u0902 \u092c\u093e\u0924 \u0915\u0930\u0928\u0947 \u0915\u0947 \u0932\u093f\u090f \u092a\u094d\u0930\u094b\u0924\u094d\u0938\u093e\u0939\u093f\u0924 \u0915\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0939\u0948 \u0915\u093f \u0915\u094d\u092f\u093e \u0909\u0928\u0915\u0940 \u0938\u094d\u0925\u093f\u0924\u093f \u0915\u0947 \u0932\u093f\u090f \u0915\u094b\u0908 \u0928\u0948\u0926\u093e\u0928\u093f\u0915 \u200b\u200b\u092a\u0930\u0940\u0915\u094d\u0937\u0923 \u0909\u092a\u092f\u0941\u0915\u094d\u0924 \u0939\u094b\u0917\u093e\u0964 \u0928\u0948\u0926\u093e\u0928\u093f\u0915 \u200b\u200b\u092a\u0930\u0940\u0915\u094d\u0937\u0923 \u0930\u094b\u0917\u093f\u092f\u094b\u0902 \u0915\u094b \u0928\u0935\u0940\u0928\u0924\u092e \u0909\u092a\u091a\u093e\u0930 \u0935\u093f\u0915\u0932\u094d\u092a\u094b\u0902 \u0924\u0915 \u092a\u0939\u0941\u0901\u091a \u092a\u094d\u0930\u0926\u093e\u0928 \u0915\u0930\u0924\u0947 \u0939\u0948\u0902 \u0914\u0930 ECD ECD \u0909\u092a\u091a\u093e\u0930 \u092e\u0947\u0902 \u0935\u0948\u091c\u094d\u091e\u093e\u0928\u093f\u0915 \u0930\u0942\u092a \u0938\u0947 \u092a\u094d\u0930\u092d\u093e\u0935\u0940 \u0938\u093e\u092c\u093f\u0924 \u0939\u094b\u0928\u0947 \u0935\u093e\u0932\u0947 \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u093e \u092e\u093e\u0930\u094d\u0917 \u092a\u094d\u0930\u0936\u0938\u094d\u0924 \u0915\u0930\u0924\u0947 \u0939\u0948\u0902\u0964 \u0907\u0938\u0915\u0947 \u092a\u0930\u093f\u0923\u093e\u092e\u0938\u094d\u0935\u0930\u0942\u092a FDA \u0928\u0947 \u0926\u094b ECD \u0909\u092a\u091a\u093e\u0930\u094b\u0902 \u0915\u094b \u092e\u0902\u091c\u0942\u0930\u0940 \u0926\u0940 \u0939\u0948         <\/p>\n<p>\u0905\u0927\u093f\u0915 \u091c\u093e\u0928\u0915\u093e\u0930\u0940 \u0915\u0947 \u0932\u093f\u090f \u0926\u0947\u0916\u0947\u0902:<\/p>\n<ul>\n<li>National Comprehensive Cancer Network (NCCN) <a href=\"https:\/\/jnccn.org\/view\/journals\/jnccn\/19\/11\/article-p1277.xml\" target=\"_blank\" rel=\"noopener\"><strong><u>Histiocytic Neoplasms, Version 2.2021, NCCN Clinical Practice Guidelines in Oncology<\/u><\/strong><\/a>\u0964<\/li>\n<li>\u092c\u094d\u0932\u0921 \u091c\u0930\u094d\u0928\u0932 \u0932\u0947\u0916, <a href=\"https:\/\/ashpublications.org\/blood\/article\/135\/22\/1929\/452713\/Erdheim-Chester-disease-consensus-recommendations\" target=\"_blank\" rel=\"noopener\"><strong><u>Erdheim Chester Disease Consensus Recommendations<\/u><\/strong><\/a><\/li>\n<\/ul>\n<p>\u092f\u0947 \u092a\u094d\u0930\u0915\u093e\u0936\u0928 ECD \u0928\u093f\u0926\u093e\u0928 \u0914\u0930 \u0909\u092a\u091a\u093e\u0930 \u092e\u0947\u0902 \u0905\u0917\u094d\u0930\u0923\u0940 \u0935\u093f\u0936\u0947\u0937\u091c\u094d\u091e\u094b\u0902 \u0926\u094d\u0935\u093e\u0930\u093e \u0932\u093f\u0916\u0947 \u0917\u090f \u0939\u0948\u0902\u0964 \u092f\u0926\u093f \u0915\u094b\u0908 \u092e\u0930\u0940\u091c \u0910\u0938\u0947 \u0921\u0949\u0915\u094d\u091f\u0930 \u0915\u0947 \u092a\u093e\u0938 \u091c\u093e \u0930\u0939\u093e \u0939\u0948 \u091c\u093f\u0938\u0947 ECD \u0915\u0947 \u092c\u093e\u0930\u0947 \u092e\u0947\u0902 \u092c\u0939\u0941\u0924 \u0915\u092e \u091c\u093e\u0928\u0915\u093e\u0930\u0940 \u0939\u0948, \u0924\u094b \u092f\u0939 \u0905\u0924\u094d\u092f\u0927\u093f\u0915 \u0938\u0941\u091d\u093e\u0935 \u0926\u093f\u092f\u093e \u091c\u093e\u0924\u093e \u0939\u0948 \u0915\u093f \u0907\u0928 \u0926\u0938\u094d\u0924\u093e\u0935\u0947\u091c\u094b\u0902 \u0915\u094b \u0909\u0928\u0915\u0947 \u0938\u093e\u0925 \u0938\u093e\u091d\u093e \u0915\u093f\u092f\u093e \u091c\u093e\u090f\u0964 <\/p>\n<p>[\/et_pb_text][\/et_pb_column][\/et_pb_row][et_pb_row _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; locked=&#8221;off&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_column type=&#8221;4_4&#8243; _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_text _builder_version=&#8221;4.27.4&#8243; _module_preset=&#8221;default&#8221; locked=&#8221;off&#8221; global_colors_info=&#8221;{}&#8221;]<\/p>\n<p><strong>\u0905\u0917\u0932\u093e&gt;<\/strong> <a href=\"https:\/\/www.erdheim-chester.org\/hi\/%e0%a4%a6%e0%a5%87%e0%a4%96%e0%a4%ad%e0%a4%be%e0%a4%b2-%e0%a4%95%e0%a5%87%e0%a4%82%e0%a4%a6%e0%a5%8d%e0%a4%b0\/\">\u0926\u0947\u0916\u092d\u093e\u0932 \u0915\u0947\u0902\u0926\u094d\u0930<\/a><\/p>\n<p>[\/et_pb_text][et_pb_text _builder_version=&#8221;4.27.6&#8243; _module_preset=&#8221;default&#8221; global_colors_info=&#8221;{}&#8221;]<\/p>\n<p><strong>\u0905\u0902\u0924\u093f\u092e \u0905\u092a\u0921\u0947\u091f:<\/strong> 03\/17\/2026<\/p>\n<p>[\/et_pb_text][\/et_pb_column][\/et_pb_row][\/et_pb_section]<\/p>\n","protected":false},"excerpt":{"rendered":"<p>ECDGA YouTube \u092a\u094d\u0932\u0947\u0932\u093f\u0938\u094d\u091f \u092e\u0947\u0902 56 \u0935\u0940\u0921\u093f\u092f\u094b \u0936\u093e\u092e\u093f\u0932 \u0939\u0948\u0902 \u091c\u093f\u0928\u092e\u0947\u0902 \u091a\u093f\u0915\u093f\u0924\u094d\u0938\u093e \u092a\u0947\u0936\u0947\u0935\u0930 Erdheim-Chester Disease (ECD) \u0915\u0947 \u0932\u093f\u090f \u0935\u0930\u094d\u0924\u092e\u093e\u0928 \u0909\u092a\u091a\u093e\u0930 \u0926\u0943\u0937\u094d\u091f\u093f\u0915\u094b\u0923\u094b\u0902 \u092a\u0930 \u091a\u0930\u094d\u091a\u093e \u0915\u0930\u0924\u0947 \u0939\u0948\u0902\u0964\u0909\u092a\u091a\u093e\u0930 \u0938\u0902\u092c\u0902\u0927\u0940 \u0928\u093f\u0930\u094d\u0923\u092f ECD \u0915\u0947 \u0932\u093f\u090f \u0909\u091a\u093f\u0924 \u0909\u092a\u091a\u093e\u0930 [&hellip;]<\/p>\n","protected":false},"author":14,"featured_media":56062,"parent":0,"menu_order":0,"comment_status":"open","ping_status":"closed","template":"","meta":{"_et_pb_use_builder":"on","_et_pb_old_content":"","_et_gb_content_width":"","cybocfi_hide_featured_image":"","footnotes":"","_links_to":"","_links_to_target":""},"class_list":["post-56009","page","type-page","status-publish","has-post-thumbnail","hentry"],"_links":{"self":[{"href":"https:\/\/www.erdheim-chester.org\/it\/wp-json\/wp\/v2\/pages\/56009","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.erdheim-chester.org\/it\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.erdheim-chester.org\/it\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/it\/wp-json\/wp\/v2\/users\/14"}],"replies":[{"embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/it\/wp-json\/wp\/v2\/comments?post=56009"}],"version-history":[{"count":27,"href":"https:\/\/www.erdheim-chester.org\/it\/wp-json\/wp\/v2\/pages\/56009\/revisions"}],"predecessor-version":[{"id":163520,"href":"https:\/\/www.erdheim-chester.org\/it\/wp-json\/wp\/v2\/pages\/56009\/revisions\/163520"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/it\/wp-json\/wp\/v2\/media\/56062"}],"wp:attachment":[{"href":"https:\/\/www.erdheim-chester.org\/it\/wp-json\/wp\/v2\/media?parent=56009"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}