{"id":113696,"date":"2026-02-01T11:11:23","date_gmt":"2026-02-01T17:11:23","guid":{"rendered":"https:\/\/www.erdheim-chester.org\/la-maladie-derdheim-chester-expliquee-symptomes-diagnostic-et-progres-de-la-recherche\/"},"modified":"2026-05-05T22:12:23","modified_gmt":"2026-05-06T03:12:23","slug":"la-maladie-derdheim-chester-expliquee-symptomes-diagnostic-et-progres-de-la-recherche","status":"publish","type":"post","link":"https:\/\/www.erdheim-chester.org\/fr\/la-maladie-derdheim-chester-expliquee-symptomes-diagnostic-et-progres-de-la-recherche\/","title":{"rendered":"Webinaire en fran\u00e7ais avec le Dr Jerome Razanamahery : d\u00e9crypter le diagnostic et les traitements de l\u2019ECD"},"content":{"rendered":"<p>Dans ce webinaire sp\u00e9cial sur l\u2019ECD, <strong>le Dr Jerome Razanamahery<\/strong>, m\u00e9decin interniste au <strong>CHU de Dijon<\/strong>, un <strong>centre de r\u00e9f\u00e9rence ECD<\/strong>, parle de la <strong>maladie d\u2019Erdheim-Chester (ECD)<\/strong>. Il explique ce qu\u2019est l\u2019ECD, pourquoi elle peut \u00eatre difficile \u00e0 diagnostiquer et comment de nouveaux traitements cibl\u00e9s contribuent \u00e0 am\u00e9liorer les r\u00e9sultats pour les patients. <\/p>\n<p><strong>Ce webinaire est pr\u00e9sent\u00e9 en fran\u00e7ais<\/strong>.<\/p>\n<p>Cette vid\u00e9o comprend un message du <strong>Pr Julien Haroche<\/strong>, m\u00e9decin r\u00e9f\u00e9rent au <strong>centre de r\u00e9f\u00e9rence ECD de l\u2019H\u00f4pital Piti\u00e9-Salp\u00eatri\u00e8re \u00e0 Paris, France<\/strong>. Il est le responsable du Centre de r\u00e9f\u00e9rence fran\u00e7ais des histiocytoses. <\/p>\n<p>La vid\u00e9o pr\u00e9sente \u00e9galement un t\u00e9moignage poignant de <strong>M. Jacques Dutu<\/strong>, qui partage avec courage son parcours avec l\u2019ECD, de la col\u00e8re et la confusion \u00e0 l\u2019espoir et \u00e0 la reprise de pouvoir sur sa vie.<\/p>\n<p><strong>Vous apprendrez :<\/strong><\/p>\n<ul>\n<li>Ce qui fait de l&rsquo;ECD un cancer du sang inflammatoire rare et complexe<\/li>\n<li>Pourquoi l\u2019ECD est difficile \u00e0 diagnostiquer pr\u00e9cocement et quels sympt\u00f4mes surveiller<\/li>\n<li>Comment des mutations comme <strong>BRAFV600E<\/strong> influencent les choix de traitement<\/li>\n<li>Comment les traitements cibl\u00e9s, tels que les inhibiteurs de <strong>BRAF et MEK<\/strong>, aident les patients<\/li>\n<li>Pourquoi le soutien en sant\u00e9 mentale et la qualit\u00e9 de vie sont importants<\/li>\n<li>Pourquoi l\u2019<strong>ECD Global Alliance<\/strong> existe et comment elle aide les patients et les familles dans le monde entier<\/li>\n<\/ul>\n<p>Cette vid\u00e9o s\u2019inscrit dans le cadre de notre mission permanente de sensibilisation, de soutien et d\u2019avancement de la recherche pour les personnes touch\u00e9es par la <strong>maladie d\u2019Erdheim-Chester.<\/strong><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Dans ce webinaire sp\u00e9cial sur l\u2019ECD, le Dr Jerome Razanamahery, m\u00e9decin interniste au CHU de Dijon, un centre de r\u00e9f\u00e9rence ECD, parle de la maladie d\u2019Erdheim-Chester (ECD). Il explique ce [&hellip;]<\/p>\n","protected":false},"author":20,"featured_media":113700,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_et_pb_use_builder":"","_et_pb_old_content":"","_et_gb_content_width":"","_wds_title":"","_wds_metadesc":"","_wds_focus-keywords":"","_wds_meta-robots-adv":"","_wds_meta-robots-noindex":false,"_wds_meta-robots-nofollow":false,"_wds_meta-robots-index":false,"_wds_meta-robots-follow":false,"_wds_autolinks-exclude":false,"_wds_canonical":"","_wds_redirect":"","_wds_opengraph":[],"_wds_twitter":[],"cybocfi_hide_featured_image":"","wds_primary_category":0,"footnotes":"","_links_to":"","_links_to_target":""},"categories":[597],"tags":[5037,5734,575,1163,5732,5733,5735,5731,5730,5027,5729,911,5021],"class_list":["post-113696","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-enregistrements-des-webinaires","tag-cancer-du-sang-rare-2","tag-dr-jerome-razanamahery","tag-ecdga-fr","tag-histiocytose-fr","tag-inhibiteurs-de-braf","tag-inhibiteurs-de-mek","tag-julien-haroche","tag-mutation-brafv600e","tag-neoplasme-myeloide-inflammatoire","tag-recherche-sur-les-maladies-rares-2","tag-sensibilisation-aux-maladies-rares-2","tag-soutien-aux-patients","tag-therapie-ciblee"],"_links":{"self":[{"href":"https:\/\/www.erdheim-chester.org\/fr\/wp-json\/wp\/v2\/posts\/113696","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.erdheim-chester.org\/fr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.erdheim-chester.org\/fr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/fr\/wp-json\/wp\/v2\/users\/20"}],"replies":[{"embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/fr\/wp-json\/wp\/v2\/comments?post=113696"}],"version-history":[{"count":1,"href":"https:\/\/www.erdheim-chester.org\/fr\/wp-json\/wp\/v2\/posts\/113696\/revisions"}],"predecessor-version":[{"id":130138,"href":"https:\/\/www.erdheim-chester.org\/fr\/wp-json\/wp\/v2\/posts\/113696\/revisions\/130138"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/fr\/wp-json\/wp\/v2\/media\/113700"}],"wp:attachment":[{"href":"https:\/\/www.erdheim-chester.org\/fr\/wp-json\/wp\/v2\/media?parent=113696"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/fr\/wp-json\/wp\/v2\/categories?post=113696"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.erdheim-chester.org\/fr\/wp-json\/wp\/v2\/tags?post=113696"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}